CARDIOLOGY Flashcards
Newborn with cyanosis, pulse oximetry changed
from 60% to 64% only on 100% oxygen
Cardiac (most likely)
Newborn with cyanosis, pulse oximetry changed
from 60% to 88% on 100% O2
Pulmonary (most likely)
What is the reason that left to right shunt lesions may not present until 1 month of age?
The pulmonary vascular resistance drops to
normal levels at that time
A 1-day-old infant with a history of maternal
diabetes, cyanosis, and tachypnea, poor response to supplemental oxygen, loud single second heart sound, no murmur, chest radiograph shows narrow mediastinum with small heart tipped on side, increased pulmonary vascularity
Transposition of great vessels
What is the next best step in a newborn with
suspected transposition of the great vessels?
Prostaglandin E1 to keep the patent ductus
arteriosus (PDA) open, followed by +/− balloon
atrial septostomy and surgery
The most common cause of cyanotic heart disease presenting a few days after birth
Transposition of the great vessels
Newborn presents with cyanosis in the lower
extremities, tachycardia, respiratory distress, and loud single S2 sound
Persistent pulmonary hypertension (R→L
shunting across the PDA)
A 1-day-old newborn presents with cyanosis,
single first and second heart sounds, chest
radiograph, shows decreased lung markings, and electrocardiogram shows left axis deviation
Tricuspid atresia with pulmonary atresia
Newborn presents with cyanosis (mother was on a medicine for severe bipolar disorder), chest radiograph shows cardiomegaly and right atrial enlargement
Ebstein anomaly
Newborn presents with severe cyanosis, systolic
ejection murmur, and a single second heart sound, chest radiograph shows decreased pulmonary vascular markings
Severe pulmonary stenosis
Newborn presents with intense cyanosis and
respiratory distress, chest radiograph shows a
“snowman” shaped heart
Supracardiac total anomalous pulmonary venous return
An 8-week-old boy presents with feeding
difficulties, poor weight gain, episodes of bluish
discoloration of the skin while feeding and crying, a harsh systolic ejection murmur (SEM) is heard over the pulmonic area and left sternal border; chest radiograph shows diminished vascularity in the lungs and diminished prominence of the pulmonary arteries, a boot-shaped heart (coeur en sabot)
Tetralogy of Fallot
During the first 48 h of life, a newborn rapidly
develops cyanosis, tachypnea, respiratory distress, pallor, lethargy, metabolic acidosis, oliguria, weak pulses in all extremities, hepatosplenomegaly, and no murmur
Hypoplastic left heart (as PDA closes)
A 2-year-old with a history of tetralogy of Fallot
has progressive agitation, increasing cyanosis, and increased fussiness
Hypercyanotic spell (Tet spell)—next step is the
knee-chest position
What is the next best step for the newborn in the previous case with suspected hypoplastic left heart?
Prostaglandin E1
A 2-week-old boy develops congestive heart
failure, severe metabolic acidosis, and poor
perfusion of the lower extremities
Coarctation of the aorta
Newborn presents with shock; the echocardiogram shows coarctation of the aorta. What is the drug of choice?
Prostaglandin E1
A 12-year-old presents with hypertension,
occasional headache, leg cramps, weak and
delayed femoral pulse, and blood pressure in the upper limb is higher than the lower limb, chest radiograph shows rib notching and scalloping on the undersurface of posterior ribs
Coarctation of the aorta
Newborn presents with shock; the echocardiogram shows coarctation of the aorta. What is the drug of choice?
Prostaglandin E1
A 12-year-old presents with hypertension,
occasional headache, leg cramps, weak and
delayed femoral pulse, and blood pressure in the upper limb is higher than the lower limb, chest radiograph shows rib notching and scalloping on the undersurface of posterior ribs
Coarctation of the aorta
A girl with Turner syndrome presents with
hypertension, weak and delayed femoral pulse
Coarctation of the aorta
Newborn infant presents with a soft, harsh systolic ejection murmur, best heard at the axillae, and precordium and no symptoms
Peripheral pulmonary stenosis (PPS)
Newborn infant presents with a soft, harsh systolic ejection murmur, best heard at the axillae, and precordium and no symptoms
Peripheral pulmonary stenosis (PPS)
The most common cardiac lesion associated with trisomy 21 (Down syndrome)
Endocardial cushion defect O. I. Naga
The most common cardiac lesion associated with Turner syndrome
Bicuspid aortic valve
The most common cardiac lesion associated with trisomy 18
Ventricular septal defect (VSD)
The most common cardiac lesion associated with Williams syndrome
Supravalvar aortic stenosis
The most common cardiac lesion associated with Noonan syndrome
Pulmonary stenosis
The most common cardiac lesion associated with DiGeorge syndrome
Tetralogy of Fallot
The most common cardiac lesion associated with Alagille syndrome
Branch pulmonary stenosis
The most common cardiac lesion associated with cri du chat syndrome
VSD
The most common cardiac lesion associated with Holt–Oram syndrome
Atrial septal defect (ASD)
The most common cardiac lesion in fetal alcohol
syndrome
VSD, ASD
The most common cardiac lesion associated with lithium teratogen
Ebstein anomaly