Scleroderma Flashcards

1
Q

Systemic Sclerosis involves what systems?

A

-skin and other body systems

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2
Q

what happens in Systemic Sclerosis?

A

=Inflamed tissue becomes hardened/ sclerotic

–>May involve kidneys (leading cause of death), lungs and vessels

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3
Q

Systemic Sclerosis is -Chronic, inflammatory, autoimmune ____ _____ disorder

A

connective tissue

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4
Q

Limited Cutaneous SSc occurs where?

A

legs, forearms, head

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5
Q

crest syndrome is associated with

A

Limited Cutaneous SSc

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6
Q

crest syndrome is

A
  • calcium deposits in skin
  • raynaud’s
  • esophageal dysfunction: acid reflux
  • sclerodactyly = thickening and hardening of the skin
  • telangiectasias = dilation of capillaries on skin causing red spider veins
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7
Q

2 types of SSC

A

limited cutaneous= legs, forearms, head

diffuse = all over

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8
Q

assessment for SSC

A
  • Joint pain
  • Joint stiffness
  • Pitting edema of hands, fingers and forearms
  • ->Edema may progress
  • Shiny skin
  • Taut/ no wrinkles
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9
Q

Diffuse SSC s/s skin/rom:

A
  • Tightening of skin
  • Hardening of skin
  • Thickening of skin
  • Loss of elasticity
  • Loss of Range of Motion
  • Ulcerations
  • Joint contractures
  • -> complete loss of function
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10
Q

Diffuse SSC organi involvemnt

A
  • GI
  • CV
  • Lung
  • Renal impairment
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11
Q

GI SSC involvement will see

A
Esophageal dysmotility
Dysphagia
Hiatal hernia
Esophagitis
Decreased Peristalsis
Malabsorption/ Diarrhea
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12
Q

CV SSC involvement will see

A

Raynaud’s

Digit necrosis/ Autoamputation of distal digits

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13
Q

Lung involvement in SSC will see

A

Pulmonary arterial hypertension

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14
Q

diagnostics for SSC

A

Similar to SLE
Response to medications helps to distinguish
Clinical presentation

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15
Q

pharmacology for SSC

A

Steroids & Immunosuppressants

Medications targeting organ disfunction

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16
Q

priority nursing intervention for SSC?

A

skin protection

17
Q

comfort measures for SSC

A
See RA interventions for joint pain/ fatigue
	Bed Cradle
	Foot board
	Room temperature
	Gloves and socks (if tolerated)
18
Q

other considerations for SSC

A

Eliminate cigarette smoke
Reduce stress
Swallow Study/ safety