Rheuma and Cardio

Question 1

features of Kawasaki Disease

Answer 1

FEVER for at least 5 days + 4 of the following features:
Conjunctivitis
Rash
Adenopathy
Strawberry tongue and other oropharyngeal changes
Hand changes

Question 2

MC od pediatric inflammatory myopathies

Answer 2

Juvenile dermatomyositis

+Gottron papules
+ heliotrope eyelids/rash
shawl sign
gower sign

severe prognostic sign: dysphagia

Question 3

MCC of nonthrombocytopenic purpura in children

Answer 3

Henoch-schonlein purpura
IgA mediated vasculitis of small vessels
linked with Nephritis: HLA B34, HLA DRB1*01
Skin biopsy: leukocytoclastic angiitis
Renal biopsy: IgA mesangial deposition

Question 4

Functional closure of the DA occurs by constriction of the medial, smooth muscle in the ductus within

Answer 4

10-15 hours after
birth.

Question 5

Anatomic closure of PDA is completed by

Answer 5

2-3wks of age

Question 6

MCC of cyanotic CHD in newborns

Answer 6

TOGA
single and loud s2
egg shaped cardiac silhoutte

Question 7

MC cyanotic heart defect beyond infancy

Answer 7

TOF
ejection click, single s2
small heart, decreased PV markings
CXR: boot-shaped heart

Question 8

cardiac defect in Down syndrome

Answer 8

Atrioventicular septal defect or endocardial cushion defect

Question 9

cardiac defect in Marfan

Answer 9

MVP, enlargement of Aorta

Question 10

cardiac defect in Hunter-Hurler

Answer 10

thickening of heart valves due to accumulation of heparan and dermatan

Question 11

cardiac defect in Noonan

Answer 11

PS

Question 12

high-pitched diastolic murmur loudest
at 3rd-4th LICS
diastolic thrill at 3rd LICS;
bounding water hammer pulse or Corrigan pulse,
wide pulse pressure

Answer 12

Aortic Regurgitation

Question 13

only pediatric condition where aspirin may be used

Answer 13

kawasaki disease
ARF

Question 14

JRA marker that indicates risk of uveitis

Answer 14

ANA