Portwine stain Flashcards
isanirregularlyshaped,redorviolaceous,macularCMthatispresentatbirthandnever disappears spontaneously.
PORTWINE STAIN
lesion
inilateral?
what part of the trigeminal what branch?
LESIONS Macular (Fig. 9-19) with varying hueso pinktopurple.Largelesions ollowa dermatomal distribution, usually unilateral (85%),althoughnotalways.Mostcommonly in the ace, in the distribution o the trigeminal nerve (Fig. 9-19), and usually the superior and middlebranches;mucosalinvolvemento con- junctiva and mouth may occur.
Hp
Revealsectasiao capillariesandnoproliera- tiono endothelialcells.GLUT-1immunoreac- tivity is negative.
does it increase as child grows?
yeah
tx
tunable dye or copper vapor lasersishighlye ective
manif
xray findings
of syndromic capillary malformation
istheassociationo PWSinthetrigemi- nal distribution with vascular mal ormations in theeyeandleptomeninges,andsuper cialcal- ci cationso thebrain.Maybeassociatedwith contralateral hemiparesis, muscular hemiatro- phy, epilepsy, mental retardation, and glaucoma andocularpalsy.Characteristiccalci cationso vascular mal ormations or localized linear cal- ci cationalongcerebralconvolutionsatx-ray.