epidermal nevus Flashcards
age when it is present.distribution
Usually present at birth or occurs in in ancy; rarely, it develops in puberty. All epidermal nevi on the head/neck region are present at birth.
Whenthelesionsareextensive,theyaretermed
systematized epidermal nevus
andwhentheyare located on hal the body, they are termed
nevus unius lateris
Linearlesionscanexhibiterythema,scaling,andcrusting,andarethencalled
infammatorylinear verrucousepidermalnevus(ILVEN)
Extensiveepidermalnevi(epidermalnevussyndrome)maybemultisystemdisordersandmaybe
associated with developmental abnormalities
bone cysts, hyperplasia o bone, scoliosis, spina bi da, and kyphosis), vitamin D-resistant rickets, and neurologic problems (mental retardation, seizures,
c o r t i c a l a t r o p h y , a n d h y d r o c e p h a l u s ) . Th e s e p a t i e n t s r e q u i r e a c o m p l e t e e x a m i n a t i o n , i n c l u d i n g t h e eyes (cataracts, optic nerve hypoplasia), and cardiac studies to rule out aneurysms or patent ductus arteriosus.
tx
Excision is the best treatment
lesion
■ Severalvariants:The verrucousepidermalnevusmaybe localized ormultiple.Lesionsare skin-colored, brown,orgrayish-brown(Fig.9-46)andarecomposedo closelysetverrucouspapules,wellcir- cumscribed; they are o ten in a linear arrangement—especially on the leg—or they may appear in Blaschko lines on the trunk