Peroxisomes and Mitochondria* Flashcards
1
Q
how is phytanic acid broken down?
A
(branched chain fatty acid) alpha oxidation
2
Q
what is long chain fatty acid broken down by and what does it produce?
A
beta oxidation and hydrogen peroxide
3
Q
what degrades h202
A
catalase
4
Q
what 3 biosynthesis does peroxisomes create
A
myelin precursor, bile acids and cholesterol
5
Q
PTS1
A
3 amino acid sequence at c terminus
6
Q
PTS2
A
less conserved sequence at n terminus
7
Q
what are the two classes of peroxisomal disease? and ie?
A
- peroxisome biogenesis disorder ie. zellweger syndrom
2. single peroxisomal enzyme deficiency ie. x linked adrenoleukodystrophy and adult refsum disease.
