Peds- GB biliary system Flashcards
3 variants of GB?
- Phrygian cap – fold at fundus
- Hartmann pouch – widening at neck
- Prominent spiral valves of Heister
6 congenital anomalies of GB?
- Ectopia
- Agenesis
- Duplication
- Biliary Atresia
- Choledochal Cyst
- Multiseptate Gb
Multiseptate GB can lead to?
- septations can lead to bile stasis and formation of gallstones
the two major causes of conjugated hyperbilirubinemia in newborns?
- liver diseases (hepatitis)
- biliary atresia
3 types of bilary atresia manifestations?
- Absence of biliary tree
- Rudimentary gb and cystic duct
- Visible gb, cystic duct and CBD
Newborns develop neonatal jaundice at what age?
3-4 weeks
Biliary atresia sono features?
- GB, cystic duct, CBD and IHBD may be seen incompletely, depending on degree of severity
- Early signs of cirrhosis
2 important findings to diagnose biliary atresia?
- triangular cord sign
- GB length <1.5 cm or absent
TRIANGULAR CORD SIGN?
Triangular, cone-shaped, fibrous ductal remnant is positioned anterior and superior to the portal vein and the hepatic artery
Biliary atresia- kasai procedure?
- Surgical intervention where a connection is made between the duodenum and gallbladder, CBD and liver to drain the bile
- Successful if performed early
- Successful in 1/3 of cases
- 2/3 will need liver transplantation
Choledochal cyst symptoms? (3)
- abdo pain
- ando mass
- jaundice
How many types of Choledochal cyst are there?
five
type 1 Choledochal cyst?
- concentric dialation of CBD
- Most common type
Type 2 Choledochal cyst?
- CBD diverticulum
Choledochal cyst type 3?
choledochocele:
- cystic dialation of intraduodenal portion of CBD
Choledochal cyst type 4?
- Ditatation of CBD with IHBD involvement
Choledochal cyst type 5?
- Caroli Disease
- Saccular dilatation of IHBD with calculus formation and bacterial cholangitis
- Minimal dilatation of IHBD, associated with hepatic fibrosis and portal hypertension
Choledochal cyst sono features?
- Cystic structure near GB continuous with bile ducts
- Large cysts containing sludge
- IHBD dilatations (type IV and V)
Choledochal cyst complications?
- Stone formation in cyst, GB, panc duct
- Biliary obstruction
- Chronic cholangitis
- Cirrhosis
- Bilirary rupture with biliary peritonitis (image)
Acquired Pathology of the Gallbladder and Biliary System (7)?
Gallbladder wall thickening Cholelithiasis Cholecystitis Hydropic Gallbladder Biliary Obstruction Sclerosing Cholangitis Rhabdomyosarcoma
Gallbladder Wall Thickness?
Normal up to 3 mm (fasting)
> 3 mm indicates disease
Gallbladder Wall Thickness inflammatory causes?
- acute and chronic cholecystitis
Gallbladder Wall Thickness noninflammatory?
- Viral hepatitis
- cirrhosis
- congestive heart failure
- pancreatitis
What is Cholelithiasis?
Presence of one or more calculi in the GB, cystic duct or CBD