PEDS Flashcards
What is stage IV-S neuroblastoma?
Children <1 yr old with specific presentation of localized primary bone marrow involvement and metastatic spread to liver an dskin
What is Sandifer’s ?
Realtes to GERd; consists of a twisting of the neck (potentially assoc with failure to thrive)
Spontaneous neonatal perforation causing free air is most likely coming from?
Greater curvature of stomach. Other causes of sudden distension secondary to intestinal perforation ar eless likely to be associated with significant itnraperitoneal hemorrhage.
How do we confirm diagnosis of ToF
Echocardiography
How do you manage cyanotic spells a/w ToF
Supplemental O2
Sedation with morphine
Beta blocker
What is a Blalock Taussig shunt
For a palliative increase in pulmonary blood flow, you can use this shutn to connect subclavian artery to the pulmonary artery
most common indication for operative repair of ToF
Increasing cyanosis and cyanotic spells
How do we close PDA?
Indomethacin by means of cyclo-oxygenase inhibition, which decreases production fo endogenous prostaglandins
How do we keep PDA open?
Prostaglandin infusion
Von Hippel Lindau
Associated with renal cell CA, renal cysts, CNS tumors, pheo
Li Fraumeni syndrome
defect in p53 – > childhood sarcomas, breast CA, brain tumors, leukemia, adrenal CA
Beckwith Weidemann
Nephroblastoma (Wilms tumor), macroglossia, visceromegaly, hyperinsulinemci hypoglycemia
McCune Albright
Bone deformities, cafe au lait, precocious puberty