Peds Flashcards
Todani classification of choledochal cysts;
MC primary malignant liver tumor in children?
Hepatoblastoma
TOF;
WAGR syndrome:
Wilms
Aniridia
Genito-urinary abnormalities
Mental retardation
2/2 deletion of short arm of chromosome 11
Tx for omental/mesenteric cysts?
Resect
Double bubble sign, maternal polyhydramnios, projectile vomiting; what does this baby have?
Duodenal atresia
1/3 of pts have Down syndrome
After a pyloromyotomy for hypertrophic pyloric stenosis, why do we perform a leak test?
To make sure no mucosal injury present and assess potency of pyloric channel
If mucosal injury is present, repair with absorbable suture, with an omental patch on top
2nd most common pediatric solid tumor and tx?
Neuroblastoma
Typically surgery
3 approaches to treat Hirschsprung disease:
Swenson
Soave
Duhammel
Swenson procedure to HD?
Pull through procedure
Aganglionic segment is resected and an end-to-end anastomosis to rectum is created
Has high risk of anastomotic stricture
Requires pelvic dissection, can lead to damage to pelvic tissues/organs
Soave procedure for HD?
Meant to avoid the extensive pelvic dissection seen with a Swenson
Removes mucosa and submucosa of rectum
Proximal bowel is attached to a cuff of rectal muscle
Duhammel procedure for HD>?
Normal proximal bowel is brought down retro-rectally and attached to the rectum in an end-to-side fashion
This creates a large anastomosis with low risk for stricture
Tx for type III choledochoceles?
ERCP + sphincterotomy
WAGR syndrome?
Deletion of short arm of chromosome 11
Wilms tumor
Aniridia
GU abnormalities
Mental retardation
TOF?
Overriding aorta
VSD
RV outflow tract obstruction
RV hypertrophy
Steps of a Ladds procedure;
Detorse volvulized bowel (counter clockwise fashion)
Cut Ladd bands before peritoneum and cecum
Appendectomy
Colon re-oriented to pts left abdomen, small bowel to patient’s right abdomen
Tx for pediatric hepatoblastoma after 4 cycles of chemotherapy?
Liver tx
4 cycles is max
Pulm sequestrations?
Extralobar vs intralobar; both tend to be found more on the left side of
Usually have no communication with bronchial tree and arterial supply is from systemic circulation