Pedi GI Flashcards
Facial defect: frontonasal and maxillary processes did not fuse. First 30-60 days of gestation.
Unknown cause
Contributing factors: Genetics, folic acid deficiency, advanced age, anticonvulsants, ETOH and smoking, family history
25% also have neuro/cardiac anomalies, club foot; 1 in 600-700 births
Cleft Lip/Cleft Palate
Surgical repair. Lip 2-6 months, early repair improves feeding.
Palate 9-18 months, essential for speech development
Cleft Lip/Cleft Palate Treatment
Careful assessment of fluid/caloric intake
Prevent aspiration/respiratory compromise
Unique approach to feeding- positioning, special feeding devices
Assess for respiratory distress, dehydration, weight gain
Control post-op pain; suture removal; prevent infection
Family support, speech therapy
Cleft Lip/Cleft Palate Nursing Considerations
Congential: 3-6 cm outpouching of lower segment of small intestine. Most common birth defect of digestive system. Most children are asymptomatic. If symptoms, usually age 1-2y. Painless rectal bleeding. “brick” or “currant jelly”- very red stool.
Can be associated with partial or complete bowel obstruction
Obstruction- younger children
Diverticulitis- older children (8y)- looks like appendicitis
Xray, U/s, CT
if symptomatic, surgical resection: ex-lap
Meckel Diverticulum
Congenital defect of abdominal wall. Internal organs eviscerate. Sac containing small intestine, colon, spleen, sometimes gonads. Giant sized is over 4.5-5 cm, contains live. Approx 775 babies/year in US. Weeks 6-11 of fetal development. Maternal risk factors: ETOH, smoking, SSRI’s, overweight/obese
High risk of cardiac defects, pulmonary hypoplasia
Treated with Silo surgery
Omphalocele
Protect, minimize fluid/temp loss (wrap with saline-soaked gauze) Pain Prevent infection Hydration/nutritional support NG tube, IV access
Omphalocele and Gastroschisis Nursing Considerations
Congenital defect of abdominal wall, life threatening. Intestines outside body via hole next to umbilicus. May also include stomach, liver. No protective sac/fluid which leads to twisting, shortening, edema.
Cause unknown.
1/3 born to teenage mothers; ETOH, tobacco
Common morbidities, feeding intolerance, NEC, FTT
Treatment is prompt surgical intervention/may be staged; silo
Gastroschisis
Incomplete formation of diaphragm, adominal contents into thoracic cavity, lung compression/hypoplasia. 1 in 2000-5000 births, females 2x more likely. 85% L sided. Severe resp distress. Intermediate intervention after birth: Ventilator, ECMO.
Surgical repair
Congenital Diaphragmatic Hernia (CDH)
ICU-level care; long hospitalizations. Family support (life-altering; 67% survival rate, long term complications). Feeding, pulmonary, re-herniation
Congenital Diaphragmatic Hernia (CDH) Nursing Considerations
esophagus does not connect to stomach (1 in 4000)
Vater (vertebral, anorectal, tracheal, esophageal, renal, radial)/ Vacterl (vertebral, anorectal, cardiac, tracheal, esophageal, renal, radial, or limb); cardiac and vertebral anomalies - 50%
Surgical correction:
Folker- streching
Jejunal interposition
Esophageal Atresia (EA)
connection between esophagus and trachea (90% with EA have TEF)
Vater (vertebral, anorectal, tracheal, esophageal, renal, radial)/ Vacterl (vertebral, anorectal, cardiac, tracheal, esophageal, renal, radial, or limb); cardiac and vertebral anomalies - 50%
Surgical correction:
Folker- streching
Jejunal interposition
Tracheoesophageal Fistula (TEF)
3 mechanisms: Decreased intake and/or increased output, increased insensible loss
Vomiting
Diarrhea
Fever, sweating, wound/tube drainage
Infants and young children especially vulnerable dehydration, (free water), volume depletion (intravascular), hypovolemia
Dehydration
3-5 % volume loss
Mild Dehydration
6-9% volume loss
S/s: tachycardia, decreased urine output, tachypnea, lower BP, delayed cap refill, irritability, thirst, restless, sunken eyes, sunken fontanel, dry mucous membranes, decreased tears
Moderate Dehydration
more than 10% fluid loss
Severe dehydration
