MTB 3 Flashcards
Which cardiac malformation requires ASD, VSD, or PDA?
Transposition b/c otherwise no oxygenation of blood
Early and severe cyanosis, single S2?
Transposition
What heart defect ass’d with Grey cyanosis?
Hypoplastic left heart syndrome
What is seen with Hypoplastic left heart syndrome?
LV Hypoplasia
Mitral valve atresia
Aortic Valve lesions
What is seen on CXR with Hypoplastic left heart syndrome?
Globular shaped heart
Pulmonary edema
Most accurate test for Hypoplastic left heart syndrome?
Echo
Severe dyspnea, early & frequent resp infxn, Single S2, peripheral pulses are bounding during first few days of life?
Truncus arteriosus
Tx for Truncus arteriosus
Surgery
Most severe sequelae of Truncus arteriosus
Pulmonary HTN
Cardiac defect early in life w/respiratory distress and severe cyanosis?
TAPVR w/obstruction
Cardiac defect age 1-2 with right heart failure and tachypnea
TAPVR w/OUT obstruction
CXR shows snowman or figure 8 sign
TAPVR w/OUT obstruction
Most accurate dx test for TAPVR w/OUT obstruction?
Echo
Treatment for TAPVR?
Surgical intervention
MCC of cyanotic heart lesion in NB?
Transposition
MCC of cyanotic heart lesion in childhood?
Tet of Fallot
Healthy child presents with holosystolic murmur and sx’s of failure to thrive?
VSD
EKG findings of VSD?
RVH
High pitched holosystolic murmur over lower left sternal border
VSD
Loud pulmonic S2
VSD
Tx for VSD
Smaller lesions close in first 1-2 yrs
Diuretics
Digoxin
Untreated VSD progresses to
CHF
Endocarditis
Pulm HTN
Fixed wide splitting of S2
ASD
Most definitive test for ASD
Cardiac cath
Increased vascular markings on CXR
VSD
ASD
Tx for ASD
Most close spontaneously
Dysrhythmias and paradoxical emboli from DVTs in adulthood
When does PDA close?
PO2 above 50 mmHg
When is PDA a normal finding?
First 12 hours of life
PDA
Wide pulse pressure
Bounding pulses
Most common complication in child w PDA
Resp Infxn
Infective endocarditis
Best initial test PDA
Echo
Most accurate test PDA
Cardiac cath
Where do Tricuspid and Pulmonary lesions radiate to?
The back
Short girl w/webbed neck, shield chest, streak gonads, horseshoe kidneys, shortened 4th metacarpal
Coarctation of the aorta
How does coarctation of aorta present?
Severe CHF
Respiratory Distress - first few months of life
Differential pulses LE and UE
Reduces pules in LE + HTN in UE
Coarctation of aorta
When is hyperbilirubinemia pathological?
Appears on 1st day of life BR Rises more than 5 mg/dL/day BR rises above 19.5 mg/dL in term child Direct BR over 2 mg/dL Persists after 2nd week of life
NB presents with hypotonia, seizures, choreoathetosis, hearing loss?
Kernicterus
TX for Pathologic jaundice
Phototherapy
If BR 20-25 -> Exchange transfusion
How does breastfeeding jaundice present?
1st week of life
Jaundice
Signs of dehydration
What is breastfeeding jaundice present?
Lactation failure
- Decreased BR elimination
- Increased enterohepatic circulation
Tx for breastfeeding jaundice present?
Alter breastfeeding to every 2-3 hours for > 10-20 mins per breast for 1st month
How does breast milk jaundice present?
Starts at 3-5 days
peaks at 2 weeks
Normal exam
Adequate breast feeding
How does esophageal atresia present?
Vomiting or choking, coughing, cyanosis with first feed
Hx of polyhydramnios
Complications with esophageal atresia?
Aspiration pneumonia - recurrent
What is seen on CXR with esophageal atresia?
Gastric air bubble
Esophageal air bubble
Coiling of NG tube
What sign is seen with pyloric stenosis?
String sign on upper GI series
- Barium swallowed and passage observed under fluroscopy
What sign is seen with Intussusception?
Doughnut sign
Steeple sign?
Croup
When do we see pyloric stenosis
First month of life - 6 months
When is a succussion splash heard?
Pyloric stenosis
sound of stomach contents slapping into pylorus
Succussion splash in adults (GI)?
When there is retained gastric contents
- Gastric outlet obstruction
- Gastroparesis
Differential DX for nonbilious vomiting?
Pyloric stenosis - projective
GERD
Infx
Metabolic derangement with pyloric stenosis?
Hypochloremic
Hypokalemic
Metabolic alkalosis
Why do we see hypochloremia and hypokalemia in vomiting?
Hydrogen lost in vomitus
Potassium loss worsens b/c of aldosterone release b/c of hypovolemia
What sign is seen on physical exam in pyloric stenosis
Olive sign - palpable mass size of olive
Epigastric
Best initial test for pyloric stenosis
Abdominal US
- thickened pyloric sphincter
Most accurate test for pyloric stenosis
Upper GI series
What 4 signs are seen in upper GI series w pyloric stenosis
- String sign - thin column of barium that leaks thru a tightened muscle
- Shoulder sign
- Mushroom sign - hypertrophic pylorus against duodenum
- Railroad track sign- excess mucosa in pyloric lumen
Tx for pyloric stenosis
- Replace IVF
- Replace electrolytes - esp K+ to decrease risk of post op apnea
- NGT to decompress bowel
- Surgical myotomy/pyloromyotomy