MTB 2 Flashcards
How does Juvenile Angiofibroma (JNA) present ?
Adolescent w epistaxis
Nasal obstruction
Visible nasal mass
Is JNA malignant or benign?
Benign - but can erode and invade local area
TX for JNA?
Remove if:
Enlarging
Chronic nosebleeds
obstructing airways
Omphalocele
Wall defect where intestines and organs form beyond abdominal wall WITH sac covering
How to screen for omphalocele?
Maternal AFP and US
Tx for omphalocele
Surgical reintroduction
What congenital disorder ass’d with omphalocele?
Edwards. 18
What do high AFP levels indicate?
NTDs
Abd wall defects
MCC for high AFP?
Incorrect dating
What is umbilical hernia ass’d with?
Hypothyroidism
Tx for umbilical hernia?
Most close by age 3.
Surgical repair at age 4.
What IS an umbilical hernia?
Weakness of rectus abdominis
vessels and bowel protrude
What is gastroschisis?
Wall defect where intestines and organs form beyond abdominal wall WITHOUT sac covering
Where is gastroschisis in relation to midline?
Lateral to midline
Tx for gastroschisis?
Immediate surgical intervention - gradual reintroduction of bowel
What age do wee see Wilms tumor?
Ages 2-5
Large palpable abdominal mass?
Wilms tumor
Presentation of Wilms tumor?
MC Asymptomatic
Hematuria, HTN, fever
Constipation, abd pain with N/V
Where does Wilms tumor metastasize to?
Lung
MC primary renal neoplasm in kids?
Wilm’s tumor