MTB 2 Flashcards

1
Q

How does Juvenile Angiofibroma (JNA) present ?

A

Adolescent w epistaxis
Nasal obstruction
Visible nasal mass

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2
Q

Is JNA malignant or benign?

A

Benign - but can erode and invade local area

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3
Q

TX for JNA?

A

Remove if:
Enlarging
Chronic nosebleeds
obstructing airways

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4
Q

Omphalocele

A

Wall defect where intestines and organs form beyond abdominal wall WITH sac covering

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5
Q

How to screen for omphalocele?

A

Maternal AFP and US

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6
Q

Tx for omphalocele

A

Surgical reintroduction

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7
Q

What congenital disorder ass’d with omphalocele?

A

Edwards. 18

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8
Q

What do high AFP levels indicate?

A

NTDs

Abd wall defects

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9
Q

MCC for high AFP?

A

Incorrect dating

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10
Q

What is umbilical hernia ass’d with?

A

Hypothyroidism

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11
Q

Tx for umbilical hernia?

A

Most close by age 3.

Surgical repair at age 4.

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12
Q

What IS an umbilical hernia?

A

Weakness of rectus abdominis

vessels and bowel protrude

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13
Q

What is gastroschisis?

A

Wall defect where intestines and organs form beyond abdominal wall WITHOUT sac covering

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14
Q

Where is gastroschisis in relation to midline?

A

Lateral to midline

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15
Q

Tx for gastroschisis?

A

Immediate surgical intervention - gradual reintroduction of bowel

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16
Q

What age do wee see Wilms tumor?

A

Ages 2-5

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17
Q

Large palpable abdominal mass?

A

Wilms tumor

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18
Q

Presentation of Wilms tumor?

A

MC Asymptomatic
Hematuria, HTN, fever
Constipation, abd pain with N/V

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19
Q

Where does Wilms tumor metastasize to?

A

Lung

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20
Q

MC primary renal neoplasm in kids?

A

Wilm’s tumor

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21
Q

Wilm’s tumor ass’d with?

A

Aniridia - malignancy

22
Q

Best initial test for Wilms tumor

A

Abd US

23
Q

Most accurate test for Wilms?

A

CT

24
Q

Deletion on chromosome 11 with large palpable abdominal mass?

A
WAGR
Wilms tumor
Aniridia
Genitourinary malformation
MR
25
Q

Tx for Wilms?

A

Total nephrectomy w/chemo and radiation

If BL kidney -> partial nephrectomy

26
Q

What age do we see neuroblastoma?

A

Usually 1st year of life

27
Q

Abdominal mass that crosses midline in infant?

A

Neuroblastoma

28
Q

Hypsarrythmia (dancing eyes) and opsoclonus (dancing feet)?

A

Neuroblastoma

29
Q

MC cancer in infants?

A

Neuroblastoma

30
Q

Dx for Neuroblastoma?

A

Increased VMA and metanephrines in urine

31
Q

How to Dx UTIs in peds?

A

Pyuria on UA and growth of 50,000 colony forming units

32
Q

TX for UTI in peds?

A

7-14 days oral Abx

33
Q

TX for 1st febrile UTI in pt < 24 mo’s?

A

Renal and bladder US

34
Q

How does Hydrocele present?

A

Painless
Swollen
Fluid-filled sac
Along spermatic cords w/in scrotum

35
Q

What transilluminates upon inspection?

A

Hydrocele

36
Q

Tx for hydrocele?

A

Usually resolves w/in 6 mos

37
Q

What is cryptorchidism?

A

Absence of one testicle

38
Q

When do we treat cryptorchidism?

A

After 1 year - orchiplexy

39
Q

Why do we do orchiplexy in cryptorchidism?

A

to avoid sterility

40
Q

What is cryptorchidism ass’d with

A

Malignancy

41
Q

What is hypospadias?

A

Opening of urethra is on ventral side of penis

42
Q

What is hypospadias ass’d with?

A

Cryptorchidism

Inguinal hernia

43
Q

Tx for hypospadias?

A

surgical correction

44
Q

Do we circumcise hypospadias?

A

NO

45
Q

What is epispadias ass’d with?

A

Urinary incontinence

bladder exstrophy

46
Q

Epispadias

A

Opening of urethra is on dorsal side of penis

47
Q

MC cyanotic heart defect in kids?

A

Tet of FAllot

48
Q

5 yo presents with SOB while playing with kids, bluish hue to his lips with frequent squatting?

A

Tet of Fallot

49
Q

Tet of fallot murmur

A

Holosystolic murmur heart best at left lower sternal border

50
Q

What effect does squatting have on preload adn SVR?

A

Increases preload
Increased SVR
R to L shunting causes increased pulmonary blood flow and increased blood oxygen saturation

51
Q

What does CXR show for tet of fallot?

A

Boot shaped heart

Decreased pulmonary vascular markings