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ABO Part 1 > MF SYNDROMES & PATHOLOGY > Flashcards

MF SYNDROMES & PATHOLOGY Flashcards

1
Q
  • Develops in 1st trimester (4 weeks) due to 1st and 2nd branchial arch
  • Condyle structure varies in severity but most severe has no TMJ
  • 2nd most common craniofacial defect (CLP is 1st)
  • Unilateral mainly but some are bilateral
  • Correct with distraction osteogenesis
  • Causes: environmental, genetic, no blood supply to 1st and 2nd arch
A

Hemifacial microsomia

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2
Q

Which syndromes have delayed eruption?

A

Aperts, Cleidocranial, Crouzons, Downs, Gardners, Progeria, or any endocrine disorders (hypo)
(NOT hemifacial microsomia)

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3
Q

Which syndromes have supernumeraries?

A

Cleidocranial dysplasia, Gardners (also CLP)

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4
Q

Osteomas, supernumerary teeth, sebaceous cysts, wormian bones, missing/hypoplastic clavicles

A

Cleidocranial dysplasia

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5
Q

Most common supernumeraries

A

Mesiodens > 3rd molars > laterals
(have them removed before ortho tx)

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6
Q

Missing teeth?

A

Ectodermal dysplasia

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7
Q

Ectopic eruption?

A

1-3% erupting into E space and canines

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8
Q

FBN1-Fibrillin 1 defect

A

Marfan Syndrome

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9
Q

F>M, occurs in 1%, can be reticular, erosive, desquamative on buccal mucosa, sores with burning or pain
Extremities: purple, pruritic, polygonal papulues

A

Lichen Planus
(NOT rheumatoid arthritis, AB treatment NO, treat with corticosteroids)

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10
Q

Hypoplastic maxilla, hyperplastic orbital rims, hypertelorism, class III, early surgery to release suture required. Coronal suture fuses at 2 years old but completely closes in adulthood.

A

Crouzon/Apert

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11
Q

Mental retardation, syndactyly, and autosomal dominant

A

Apert ONLY

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12
Q

Fusion of coronal suture (Bradyocephalic)

A

Crouzon

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13
Q

Coronal + Metopic + Sagittal (Dolichocephalic)

A

Apert

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14
Q

Neural crest cells fail to migrate to first and second branchial arch = both maxilla and mandible hypoplastic. NO mental retardation. Ear malformation, retruded mandible very obtuse with large antegonial notch, malar deficiencies, downward sloping eyes

A

Treacher Collins

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15
Q

Retrognathic mandible (hypoplastic/severe), posterior tongue position, respiratory problems (cyanosis at birth), lack of chin, prominence, cleft palate NOT cleft lip

A

Pierre Robins

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16
Q

Mental retardation, vascular problems, macroglossia, Class III, narrow arch, crossbites, periodontal disease, more likely to develop leukemia, simian crease in hand

A

Down syndrome

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17
Q

Autosomal dominant, occurs in 1:8000, affects both primary AND permanent dentition, blue sclera

A

Dentinogenesis Imperfecta

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18
Q

Drooping lower lip?

A

Facial nerve damaged

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19
Q

Paresthesia?

A

Inferior alveolar nerve damaged

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20
Q

Cause by pituitary adenoma, increase in growth hormone after fusion of epiphyseal plate, large sella and frontal sinus is affected more (causes frontal bossing)

A

Acromegaly

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21
Q

Increase in growth hormone before fusion of epiphyseal plates, large pituitary gland, mandibular prognathism

22
Q
  • More infectious: Hep B or HIV?
  • Vaccines for Hep B (DNA) and Hep C (RNA)?
A
  • Hep B (difficult to contract HIV)
  • Hep B vaccine, Hep C no vaccine
    Most are asymptomatic
23
Q

Patients have weekly injection of interferon; epidemiology RNA

24
Q

Missing tooth and derived from enamel organ; does not have keratin lining like OKC

A

Primordial cyst

25
25-40% associated with unerupted tooth and derived from dental lamina
OKC
26
Posterior mandible, scalloping between teeth (well defined borders), no epithelial lining, unicystic
Traumatic/simple bone cyst
27
Uncommon odontogenic tumor, posterior mandible, radical resection of affected bony segment, unicystic are less common and less affressive than multicystic, 1% of all oral tumors, 18% of odontogenic tumors
Ameloblastomas
28
Pupil dilation and vessel constriction
Amphetamines
29
Mu, kappa, delta receptors, pupil constriction
Opioids
30
______ resorption on endo-treated teeth than normal vital teeth. Can be moved ______. Most likely related to history of resorption if pre-existing or length of treatment during; NOT gender related (Houston)
- Less - Immediately
31
- Condition that causes root resorption? - Worst place to have RR? - Most common in… - Severe is defined as…
- Shamoshima, hypothyroid, hypoparathyroid, IL-B - Upper lateral incisors - Hispanics > Caucasians > Asians - 4mm or 1/3 of original root length
32
Apexification: _______ root fracture
Increased
33
Best way to treat 1 wall defect
Extrude/upright
34
Bonds to hyproxyapatite in bone and inhibits resorption - Parenteral vs oral? Prevent relapse, determine if osteonecrosis by radiograph, decreases osteoclast activity, effect on osteoblasts is they can’t function in inflammatory environment
Bisphosphonates - Parenteral contraindicated - Oral okay
35
Midfacial cleft/Ora-facial clefting
Hypertelorism
36
Syndrome occurs in the 1st stage of craniofacial development
Fetal Alcohol Syndrome
37
2nd stage?
Anencephaly
38
3rd stage
Hemifacial/Treacher Collins
39
4th stage
CL/CP
40
5th stage
Aperts/Crouzons
41
Failure to fuse **median nasal process** and **maxillary process**
CL/P - Lip 6 weeks, Palate 8-10 weeks
42
- Lip closure? - Alveolar graft? - Missing teeth? - Most common in… - Prevalence?
- 3 months old - 1/2-2/3 root development of canine - Upper Bs most common - Native American > Asian > Caucausian > AA - 1:700 CL/P
43
Failure to fuse sagittal suture, dolichocephalic head - long AP
Scaphocephaly
44
Most common benign salivary tumor
Pleomorphic adenoma
45
Most common odontogenic tumor
Odontoma
46
Hemophilia A or B more common? Give tylenol for pain, no premedication for ortho, but yes for extractions
Hemophilia A
47
No antibiotic prophylaxis for…
Mitral valve prolapse
48
Premedication?
- 1 hr before (2g Amoxicilin or 600mg Clindamycin) - History of infective endocarditis - Banding, removal, and TADs
49
Increase in lower facial height, lip apart posture, narrow alar base, and self-reported mouth breathing. Intraorally, clinicians see narrow maxillary arch with high palatal vault and a posterior crossbite with a Class II dental malocclusion
Adenoid facies (long face syndrome)
50
Bilateral anterior open bite?
Osteoarthritis/degenerative arthritis
51
Unilateral posterior open bite, shift to affected side, seen in young women, unknown cause but could be due to estrogen dysfunction
Idiopathic condylar resorption

ABO Part 1 (14 decks)

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