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Pulomonary HTN
Takayasu Arteritis (pulseless disease) - due to pulmonary a. dz.
Pulsus paradoxus
Adhesive Mediastinopericarditis
Oral aphthous ulcers, Genital ulcers, Uveitis
Behcet Disease
pulm capillaritis
Microscopic Polyangiitis (leukocytoclastic vasculitis/ hypersensitivity vasculitis)
type of nevus flammeus that thickens skin surgace and not fade over time
port wine stain
MI
Takayasu Arteritis (pulseless disease) -due to coronary involvement
pitting edema
R sided HF
cyanosis in LE
coarctation of aorta w PDA
Raynaud like cold sensitivity
Thromboangiitis Obliterans (Buerger Disease)
LVH –> LAH –> afib –> thrombosis
L-sided HF
weak pulse in LE
AAA
polycythemia
R–>L shunt
Can cause compression syndromes, especially in the brain in VHL disease (cerebellum, brainstem, retina, pancreas and liver lesions).
Cavernous Hemangioma
transverse myelitis
aortic dissection if vert aa’s affected
pulsating mass in abd
AAA
‘Peau d’orange’
lymphedema
-d/t persistent edema and deposition of interstitial CT (common in breast cancer) when draining lymphatics are clogged with tumor cells
ring-like opacities on CXR
calcific stenosis of bicuspid aortic valve
ball-valve obstruction of AV valve
myxoma, lipoma
Trousseau sign
Migratory Thrombophlenitis
-Venous thromboses appear in one location, disappear and occur at another site
patches and plaques on the skin, mucous membranes, LNs, GI tract of viscera
aids assoc (epidemic) KS
- Facial port wine nevi.
- Ipsl. venous angiomas of cortical leptomeninges.
- Mental retardation.
- Seizures.
- Hemiplegia.
- Skull radioopacities.
port wine stain assoc w Sturge-weber syndrome (encephalotrigeminal angiomatosis)
patches and plaques on the LN and cutaneous
endemic af KS
renal fialure
malig HTN
chronic sinusitis
Granulomatosis with Polyangiitis (Wegener Granulomatosis)