L7: developmental conditions pt 2

Question 1

what is the disease where there is abnormal bone tissue in jaw

Answer 1

cherubism

Question 2

in cherubism, bone is replaced by what

Answer 2

by soft tissue rich in fibroblasts and multi nuclear giant cells

Question 3

what are oral manifestations of cherubism

Answer 3

• bilateral enlargement of mandible/ maxilla
• cause rounded face and swollen cheeks

Question 4

what disease will have upward looking eyes

Answer 4

cherubism

Question 5

what dental features are seen in cleidocranial dysplasia

Answer 5

• supernumerary teeth
• delayed appearance of secondary teeth
• peg like teeth
• misalignment of teeth

Question 6

what are some systemic features of cleidocranial dysplasia

Answer 6

• shortened or absent clavicles **8
• delayed closure of fontanels
• presence of craniofacial, skeletal anomalies
• short stature

Question 7

name 3 developmental conditions with hard tissue findings

Answer 7

1) Cherubism
2) Cleidocranial dysplasia
3) Nevoid basal cell carcinoma syndrome (gorlin)

Question 8

what is another name for nevoid basal cell carcinoma syndrome

Answer 8

gorlin syndrome

Question 9

what systemic manifestations are in gorlin syndrome

Answer 9

• pits on palms of hands, soles of feet
• calcium deposits in brain
• skeletal abnormalities – bifid ribs
• large head

Question 10

what oral manifestations are in gorlin syndrome

Answer 10

• jaw cysts
• benign tumours in jaw
• cleft lip/ palate

Question 11

effects of hypothyrid can be reversed if picked up early. if we dont intervene early, children can get ____

Answer 11

global developmental delay (GDD)

Question 12

what is the difference between natal and neonatal teeth

Answer 12

natal = born with it
neonatal = get witin 30 days

Question 13

features of an oral melanocytic macule

• is it symptomatic
• solitary or multiple
• borders?
• colour
• shape and size
• does it darken

Answer 13

• asymptomatic
• solitary
• well circumscrbed
• uniformly brown
• round or oval lesion <1cm
• does not darken with sun

Question 14

where are oral melanocytic macules usually found in oral cavity?

Answer 14

on labial/buccal mucosa, gingival and palate
- if on lower lip vermillion, it is most likely pigmented lesion

Question 15

histology of oral melanocytic macule

Answer 15

increase production/deposition of melanin in the basal cell layer and
lamine propria or both without increase in melanocytes

Question 16

features of benign migratory glossitis
- one or a few patches?
- borders?

Answer 16

• multiple
• well demarcated areas of erythema (due to atrophy of filiform papillae)
• surrounded partially or completely by slightly elevated, white scalloped borders

Question 17

location of benign migratory glossitis

Answer 17

frequently on the anterior two thirds of the dorsum of the tongue, less commonly in other locations

might be found in buccal/labial mucosa or floor of mouth