IS DAY 4 Flashcards

1
Q

MORE THAN HALDF OF IMMUNOGLOBULINEMIA

A

B CELL DEFICIENCIES

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2
Q

AB FAIL TO DEVELOP OR ABSENT IMMNUOGLOBULIN
PRE B CELL DID NOT MATURE
ABSENT B CELL IN BM AND PERIPHERAL BLOOD
NO GAMMA REGION IN ELECTROPHORESISS

A

BRUTON AGAMMAGLOBULINEMIA

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3
Q

NORAML TOTAL IG

A

COMMON VARIABLE HYPOGAMMAGLOBULINEMIA

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4
Q

MOST COMMON COGENITA IMMUNODEFICIENCY
MHC 3 DELETION
PRODUCTION OF ANTI IGA +IGA

A

SELECTIVE IGA DEFICIENCY

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5
Q

INADEQUATE IMMUNE REACTION TO TEH. INFECTION WITH EBV

A

X LINKED LYMPHOOPROLIFERATIVE DISEASE

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6
Q

HIGH IG, LOW IGG AND IGA, HEMOLYTIC ANEMIA, THROMBOCYTOPENIA AND NEUTROPENIA

A

HYPER IGM

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7
Q

HIGH IGE AND IGD —-STAPHYLOCOCCAL INFECTION

A

HYPER IGE

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8
Q

DEFECT IN MHC CLASS 1 AND/ OR CLASS 2

A

BARE-;YMPHOCYTE SYNDROME

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9
Q

MOST SERIOUS CONGENITAL IMMUNE DEFICIENCY ADA DEFICIENCY

A

SCID) SEVERE COMBINED IMMUNNODEFICIENCY

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10
Q

MUTATION GENE ENCODING FOR WAS PROTEIN WHICH PLAY A ROLE IN ACTIN
ABSENCE OF ABOUT IGM IS THE MOST CONSISTENT LAB FINDING

A

WAS) WISKOTT-ALDRICH SYNDROME

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11
Q

T CELL RECEPTOR REARRANGEMENT DOES NOT OCCUR
CHROMOSOME 7 AND 14 BREAKAGE

A

ATAXIA-TELANGIECTASIA

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12
Q

CD4 IS PRIMARY TARGET

A

AIDS

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13
Q

OPPORTUNISTIC INFECTION OF AIDS

A

P CARINII

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14
Q

CD4 AND CD8 RATIO FOR AIDS PX

A

2:1 TO 0.5:1

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15
Q

3 STAGES OF AIDS
MONTHS TO YEARS FLU LIKE SYMPTOMS ASYMPTOMATIC

A

PRIMARY

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16
Q

ARC HAS PHYSICAL SYMPTOMS BUT NO OPPURTUNISTIC PATHOGEN OR INFECTION

A

INTERMEDIATE

17
Q

2-10 YEARS AND HAS OPPURTUNNISTIC PATHOGEN

A

FINAL STAGE AIDS