Idiopathic Pulmonary Fibrosis Flashcards
1
Q
What is the histological pattern seen in idiopathic pulmonary fibrosis?
A
Usual interstital pneumonitis (interstitial inflammation and fibrosis at varying stages of development)
2
Q
What is the prognosis of IPF?
A
Inevitable progression to end-stage lung disease (mean survival 3 years)
3
Q
How is IPF treated?
A
GCS
Pirfenidone
IFN-y 2B
Oxygen
4
Q
Pirfenidone
A
TGF-B inhibitor