GU

Question 1

Most common tumor of infancy

Infants

Answer 1

Wilms tumor,
Staged 1,2,3,4,5. Stage 5 is bilateral and requires independent classification
Stage 3= Needle track of the fucking resident.

Question 2

Wilms tumor

Answer 2

If bilateral = NEPHROBLASTOMATOSIS

Average age 3

Overgrowth syndrome:
Beckwith Wiedemann= Omphalocele, macroglosia, hepatoblastoma
Sotos= Retarded, Macrocephaly and ugly

Non Overgrowth syndromes:
WAGR: Wilms, aniridia, genital, growth retarded.
Drash: Wilms, pseudohermafroditism, progressive glomerulonephritis.

WILMS NEVER OCCURS BEFORE 2 MONTHS OF AGE.

Question 3

Born with it and associated with bilateral Wilms

Answer 3

Nephroblastomatosis
Picture of nephroblstomatosis + Wilms
Screening ultrasound every 3 months until patient turn 8

Question 4

Newborn with a hypoechoic lesion on ultrasound

Answer 4

MESOBLASTIC NEPHROMA.

Wilms like tumor, but <1 month old.

Solid renal tumor of infancy. Fetal hamartoma. Most common renal tumor in the first month of life.Involves renal sinus.

Question 5

Macroscopic cysts without communication (unable to excrete into collecting system)

Answer 5

MULTICYSTIC DYSPLASTIC KIDNEY
0-3
Benig

Question 6

Associate dwith DICER 1 mutation and herniates to renal pelvis

Answer 6

MULTILOCULAR CYSTIC NEPHROMA (Dicer 1 MUTATION: pleuropulmonary blastoma)
Herniates to the renal pelvis
No solid component or necrosis.
Michael Jackson tumor (boys and young girls)
4 year old.

Question 7

Most common solid tumor of adolescents (>10 )

Answer 7

Renal cell carcinoma

Question 8

What RCC is associated with translocation

Answer 8

AFter exposure to chemothreapy

Most common subtype in adolescents

Question 9

Sickle cell TRAIT

Answer 9

Medullary subtype RCC

Question 10

VHL/Renal cancer

Answer 10

Clear cell type RCC

Question 11

What is the most common bladder malignancy in kids

Answer 11

Rhabdomyosarcoma

• 20% mets
• 20% ocurre in the bladder or prostate region
• Most of the rhabdos are actually in the orbit or nasopharynx.
• Bimodal 2-4 and 15-17
• Li Fraumeni cancer and NF1
• Paratesticular tumors are the only genitourinary tract rhabdomyosarcomas that tend to occur in older children, typically adolescents.

Question 12

Most common benign bladder lesion in pediatrics?

Answer 12

Papillary urothelial neoplasm of low malignant potential (PUNLMP)

Question 13

Paratesticular mass in young adolescent

Answer 13

Paratesticular rhabdomyosarcoma