final exam-Table 1 Flashcards

1
Q

What are 2 important diagnostic tests for anemia?

A

Reticulocyte count, Hgb

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2
Q

What does a high retic count with high bilirubin indicate?

A

Bone marrow is working!

Most likely d/t destruction or loss of RBCs (hemolytic)

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3
Q

(acute/chronic) anemias are well tolerated in children

A

Chronic

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4
Q

Anemic disorder characterized by bone marrow aplasia

A

Diamond Blackfan anemia

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5
Q

Your patient presents with anemia + Petechiae. You suspect:

A

Leukemia or HUS

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6
Q

Which lab would show you the presence of spherocytes?

A

Peripheral blood smear

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7
Q

When does Fe deficiency anemia first appear?

A

After the first 4-5 mo of life

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8
Q

What should you check if a pt presents with neutropenia or thrombocytopenia?

A

Bone marrow fxn

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9
Q

Name the iron studies for Fe Deficient anemia

A
Serum ferritin (low)
Serum iron (low)
Total iron binding capacity (inc)
Transferrin saturation  (low)
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10
Q

B-12 deficiency is a common finding in this GI disorder

A

Crohn’s

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11
Q

Smooth beefy red tongue may indicate

A

B-12 deficiency

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12
Q

Fanconi and Diamond-Blackfan anemias are ____ forms of normocytic anemia

A

Congenital

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13
Q

____ can cause acquired normocytic anemia

A

Parvo B19

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14
Q

What is TAR and what condition is it found in?

A

Thrombocytopenia with absent radius. Fanconi anemia

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15
Q

Spherocytosis is inherited this way

A

Autosomal Dominant

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16
Q

____ anemias are characterized by Anemia, Jaundice, Splenomegaly

A

Hemolytic

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17
Q

Longstanding spherocytosis and sickle cell disease can cause _____

A

Gallstones

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18
Q

What is the most common inherited enzyme defect?

A

G6PD deficiency

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19
Q

G6PD commonly presents with this finding

A

Hyperbilirubinemia

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20
Q

This hemoglobinopathy is found in carriers only

A

Thalassemia trait

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21
Q

Thalassemia minor is a type of _____ thalassemia

A

Beta

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22
Q

Hemophilias, vitamin K deficiency, and DIC are all disorders of _____

A

Coagulation

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23
Q

Intrinsic clotting pathway is measured by a

A

PTT

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24
Q

Extrinsic pathway measured with a

A

PT

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25
Q

A pt who is bleeding into their joints should be worked up for

A

Hemophilia

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26
Q

More common mechanism of thrombocytopenia

A

Increased consumption/ breakdown of RBCs

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27
Q

____ is a type of thrombocytopenia associated with severe illness or shock

A

DIC

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28
Q

Most common bleeding disorder of CHILDhood

A

ITP

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29
Q

ITP usually shows up after____

A

A viral infection

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30
Q

Treatment for ITP includes

A
Steroids
IV Ig (in severe cases)
31
Q

Factor ___- and Von Willebrand work together

A

VIII

32
Q

_____ is the most common INHERITED bleeding disorder among Caucasians (though it can be acquired…)

A

Von Willebrand disease

33
Q

VW disease can be treated with _________, which releases vWF from endothelial stores

A

Desmopressin

34
Q

FFP contains____

A

All coag factors

35
Q

If you have abnormal PT/PTT, you would give

A

FFP

36
Q

If you have normal PT/PTT values, you would give

A

Cryoprecipitate

37
Q

Clotting problems are (more/less) common in kids than adults

A

Less

38
Q

First labs for a CA workup

A

CBC w/ diff

Peripheral blood smear

39
Q

ALL occurs most commonly in kids aged _____-______

A

2-10 (peak at 4)

40
Q

Most common CA treatment for kids

A

Chemo

41
Q

Philadelphia chromosome is associated with ____

A

CML

Chronic Myelogenous Leukemia

42
Q

Pt presents with firm, non-tender lymph node and hx cough. What do you order?

A

CBC
CXR
Lymph biopsy

43
Q

Hip dysplasia (is/is not) a disease of dislocation

A

Is NOT

44
Q

____ is the abnormal relationship between the proximal femur and acetabulum

A

Hip Dysplasia

45
Q

Hip dysplasia can be diagnosed using these techniques

A

Barlow’s and Ortolani’s maneuvers

46
Q

______ are indicative (not diagnostic) of hip dysplasia, occurring in up to 40% of cases

A

Asymmetric Skin folds

47
Q

Radial head subluxation is also known as

A

Nursemaid’s Elbow

48
Q

Typical posture associated with radial head subluxation

A

“my arm” posture

49
Q

Torus fractures are also known as

A

Buckle fracture

50
Q

Torus fractures affect these bones

A

Radius/ulnar

51
Q

___ is an oblique fracture of the distal tibia without a fibula fracture

A

Toddler’s Fracture

52
Q

Salter Harris classification describes ______ fractures

A

Epiphyseal

53
Q

A type _____ S-H fracture through a portion of the physis and epiphysis into the joint that may result in complication because of intra-articular component and because of disruption of the growing or hypertrophic zone of the physis.

A

Type III

54
Q

A type ____ S-H fracture presents as a crush injury to the physis with a poor functional prognosis

A

Type V

55
Q

This type of S-H fracture has joint involvement

A

Type III

56
Q

Most common bone tumor in children (benign)

A

Osteochondroma

57
Q

Most common malignant bone tumor in children

A

Osteosarcoma

58
Q

Anterior thigh and knee pain may be presentations of a ___ problem

A

Hip

59
Q

Joint pain can be an early presentation of ___-

A

Crohns Disease

60
Q

____ is the inflammation at the insertion of a ligament to a bone

A

Enthesitis

61
Q

You order an ANA on your patient. It comes back positive. What should be on your differential?

A

Lupus

62
Q

Most common site of pauciarticular arthritis

A

Knee

63
Q

___ often presents with a cyclic fever, salmon pink macular rash, and HSM

A

Systemic Form of JRA

64
Q

The 3 P’s of systemic JRA

A

Polyserositis
Pleuritis
Pericarditis

65
Q

First lab to order for suspected SLE

A

ANA

66
Q

Mainstay treatment for SLE

A

Steroids

  • methylprednisolone/ prednisone
  • hydroxychloroquin
  • NSAIDs
67
Q

Most common vasculitis in childhood

A

Henoch Schonelien Purpura

68
Q

Most likely cause of HA in kids

A

Migraine or tension HA

69
Q

Which of the following is NOT a test for MONO

A

CBC w/ diff
Antibodies
IGM
Viral swab

70
Q

2yo w/ fever, dyspnea, sniffing dog position.

Swelling stops at midline

A

GROUP A STREP

retropharyngeal abscess

71
Q

RSV

A

Synagis is given as prophylaxis

72
Q

9 y/o Suspected URI, x-ray shows hyperinflation

A

Albuterol trial

73
Q

5 y/o amox w/ rash (erythema multiforme)

A

Oral antihistamines