Falcon Review Pediatrics 3 Flashcards
A patient presents with a history of sweating while feeding, what pathology does this suggest
Suggestive of cardiac disease
What physical exam findings are suggestive of cardiac disease pediatrics
Poor growth or failure to thrive Abnormal heart rate blood pressure Crackles suggest of left-sided failure Hepatomegaly suggestive of right-sided failure Cyanosis or clubbing Murmur
What is the best diagnostic test for pediatric cardiovascular disorders
Echocardiography
Other studies are helpful such as chest x-ray EKG MRI and cardiac catheterization
Generally speaking define innocent murmurs
Usually soft
Never just diastolic
Never associated with a thrill or a click
Do not require additional work up
Name the four major types of innocent murmurs
Stills
Pulmonary flow murmur
Pulmonary ejection murmur
Venus hum
Describe a stills murmur
3 to 6 years old
Soft vibratory or musical systolic ejection murmur heard at left lower to mid sternal border
Describe a pulmonary flow murmur
0 - 6 months of age
High-pitched blowing systolic murmur at upper left sternal border due to turbulent flow at the origin of the right and left pulmonary arteries
Transmits to back and axilla
Define pulmonary ejection murmur
Similar to pulmonary flow murmur
8 to 14 years of age
Blowing early systolic murmur at upper left sternal border due to increased flow over the pulmonary valve
Define a Venus hum
Not a true murmur
3 to 6 years of age
Continuous (starts in systole and spills into diastole) murmur
Heard in supraclavicular or infraclavicular areas, disappears with compression of jugular vein Institute and supine position
What other concerns should you have for a patient with a congenital heart disease
30% of patients will have other anatomic abnormalities
What are the common causes of cyanosis
Cardiac
Pulmonary
Hematologic
Neurologic
What is the best test isolates the cause of cyanosis
Hyperoxia test
What are the expected results for cardiac disease causing cyanosis on the hyperoxia test
Before oxygenation less than 40 PaO2
after oxygenation less than 50 PaO2.
With complete mixing before you have 50 PaO2 after oxygenation you’ll have less than 150 PaO2
What valves open with systole
Aortic and pulmonic
What valves close with systole
Tricuspid and mitral
What is the most common congenital heart malformation
VSD
Ventricular septal defect
Will a large or small ventricular septal defect have a soft murmur
large
What are the symptoms of a large ventricular septal defect
Congestive heart failure Active precordium Hepatomegaly Crackles BVH or LVH
What is Eisenmenger’s physiology
Initially there is a left to right shunt
Then right ventricular hypertrophy and increased pulmonary vascular resistance
Then a right to left shunt develops
Blood is bypassing lungs and leads to cyanosis
What murmur is highly suggestive of a the ventricular septal defect
Holosystolic murmur (Harsh or soft) at lower left sternal border
What is the prognosis of a ventricular septal defect
30 to 50% of cases will close spontaneously by two years
Surgical closure for failure to close and large defects
What is the normal cardiac to rib cage ratio
Less than 0.5
When does pulmonary vascular resistance reached its nadir in pediatrics
Eight weeks
You will begin to get an increase in left to right shunting
What is the most common type of ASD
Ostium secundum type
Most patients with ASD or asymptomatic until when
Third decade of life
What murmur is suggestive of an atrial septal defect
Systolic ejection murmur and left mid and upper sternal border,
Wide fixed split S2 due to an increased blood in the right atrium and ventricle being pushed through the pulmonic valve
Discuss normal physiology of a split S2
With inspiration the pulmonic valve closes a little later
What many seen on X-ray with an atrial septal defect
An enlarged right atrium in ventricle
What is the biggest risk factor for endocardial cushion defect
Trisomy 21
What murmur is associated with endocardial cushion defect
Holosystolic murmur heard at apex (AV valve insufficiency)
What is a PDA
Patent ductus arteriosus
Failure of closure of ductus resulting in blood flow from aorta to pulmonary artery
Common in prematurity
What symptoms are associated with a large PDA
Pulmonary overload
Wide pulse pressure
Bounding arterial pulses
In infants what may be used to help close the PDA
Indomethacin
prostaglandin inhibitor
What cardiac malformation is highly associated with Turner’s syndrome
Coarctation of the aorta
What murmur is associated with coarctation of aorta
Short systolic murmur at the left upper sternal border with radiation to left back
What chest x-ray findings are associated with coarctation of the aorta
Marked cardiac enlargement
Increased pulmonary vascular markings
Rib notching (from enlarged collaterals)
What congenital malformations are associated with cyanotic heart disease
The five T’s
Truncus arteriosus Transposition of the great arteries Tricuspid atresia Tetrology of Fallot Total anomalous pulmonary venous return
Pulmonary atresia
Large VSD
The last two or associated with cyanotic heart disease after Eisenmenger’s physiology
What’s the most common cause of congenital cyanotic heart disease
Tetralogy of Fallot
What are the findings associated with tetralogy of Fallot
Ventricular septal defect
Pulmonary stenosis
Hypertrophy of right ventricle
Overriding aorta
What determines the cyanotic yet spells associated with Tetralogy of Fallot
Ventricular pressure determines the direction of bloodflow
Acyanotic tetralogy is associated with sufficient pulmonary bloodflow shunting across the VSD is balanced
Paroxysmal cyanosis tet spells occur when systemic resistance drops or pulmonary resistance increases
What will reverse the paroxysmal cyanosis associated with pathology of Fallot
Increasing the left side pressures will reverse the right to left shunt such as bringing the knees to the chest or squatting
What are the murmurs associated with tetralogy of Fallot
VSD over the lower left sternal border
Pulmonic Stenosis
What chest x-ray finding do you expect to have with tetralogy of fallot
Boot shaped heart
What is the transposition of great vessels
Aorta arises from right ventricle, pulmonary artery arises from left ventricle resulting in a parallel circulation
Must be some communication atrial, septal or ductal levels to be compatible with wife
What is the most common cause of extreme cyanosis within the first 24 hours of life
Transposition of the great vessels
Will the cyanosis correct with oxygenation for a transposition of the great vessels
No
What is the treatment for transposition of the great vessels
Prostaglandin to maintain ductus open is life-saving used PGE
Surgical correction is definitive
What do you expect to find with pulmonary atresia on EKG
Tall spiked P waves suggestive of right atrial enlargement, right ventricular hypertrophy
What is the treatment for pulmonary atresia
Maintain ductus open until surgery
What murmur is associated with pulmonary stenosis
Harsh systolic ejection murmur with ejection click at left upper sternal border
What findings suggestive of tricuspid atresia
Cyanosis at birth
Systolic murmur along left sternal border
Single S2
Left axis deviation in the infant
What findings on X-ray are suggestive of a total anomalous pulmonary venous return
The snowman or figure 8 with cardiomegaly
What murmur is associated with total anomalous pulmonary venous return
Systolic murmur at left upper sternal border
S2 fixed and widely split
Increase flow over the pulmonic valve will cause what heart sound
Split S2
What is truncus arteriosus
Single vessel arises from the ventricles supplying systemic/pulmonary/coronary circulation
What the complications of a hypoplastic left heart
Inadequate systemic circulation and pulmonary venous hypertension
Small aorta
What is the most common cause of myocarditis
Viral etiology is most common enterovirus (coxsackie) virus and adenovirus
What are the causes of a dilated cardiomyopathy in infants
Often idiopathic
Maybe associated with neuromuscular disease, drug toxicity, and chemotherapy (including doxorubicin)
What is the diagnostic study for cardiomyopathies
Echocardiogram
What causes acute rheumatic fever
GABHS
1 to 3 weeks after preceding streptococcal infection is commonly in 5 to 15-year-olds
What is required to diagnose acute rheumatic fever
The Jones criteria
- Must have two major criteria or one major and two minor criteria plus evidence of preceding strep infection
What are the Major Jones criteria
Carditis Arthritis Erythema marginatum Chorea Subcutaneous nodules
What are the minor Jones criteria
Fever arthralgia elevated acute phase reactants Prolonged ER Previous rheumatic fever
What is the treatment for acute rheumatic fever
Treat streptococcal infection and monthly penicillin prophylaxis
Salicylates to decrease myocardial inflammation
Steroids for carditis
What is a complication of acute rheumatic fever
Valvular heart disease
What are the most common organisms that cause endocarditis
Staff aureus
Streptococcus Viridans
What are the signs and symptoms of endocarditis
Acute or insidious onset
Persistent fever, chills, arthralgias, new murmur, petechiae
Oslers nodes (painful)
Janeway lesions (painless) splinter hemorrhages
How is endocarditis diagnosed
Echocardiogram
What preventative measures must be taking with endocarditis
Prophylactic antibiotics prior to dental visits
How is hypertension diagnosed in pediatrics
What pressure above 95% for age 3 review measurements
What is the most common cause for pediatric hypertension
Most commonly secondary
Renal is 75 to 80%
What are the risk factors for pediatric arrhythmias
Congenital, acquired or functional heart disease Electrolyte abnormalities Drug toxicity Poisoning Collagen vascular disease
What are some causes of sinus bradycardia pediatrics
Increased vagal tone
hypothyroidism
increased intracranial pressure
anorexia nervosa
Most commonly a normal finding in healthy athletic children
What is the difference between a Mobitz type I and a Mobitz type II heart Block
Type one will have a prolongation of PR then a drop a QRS
Type II will just drop the QRS
What maternal diseases associated with a third degree heart block in infancy
Maternal lupus
What are the causes of sinus tachycardia
Hypovolemia Shock Anemia Fever Sepsis Pulmonary embolism Medications
What do you expect to see on an EKG for supraventricular tachycardia
A runn of three or more premature supraventricular beats a greater than 230 beats permitted
Abnormal or absent P waves
Key association with WPW syndrome
What is WPW syndrome
Anomalous conduction pathway to ventricles bypassing the AV node which leads to premature and prolonged depolarization of ventricles
Predisposes to SVT
On the EKG: shortened PR, Delta wave, wide QRS
What is the treatment for long QT syndrome
Beta blocker
What is apnea of prematurity
Premature infants less than 36 weeks of gestation holding their breath for periods of less than 15 seconds
What is the treatment of apnea prematurity
Theophylline/caffeine as central stimulant
What is the obstructive sleep apnea
Prolonged partial airway obstruction intermittent cessation of breathing disrupting sleep and breathing
What are the pediatric risk factors for obstructive sleep apnea
Adenotonsillar hypertrophy
trisomy 21
Anatomical abnormalities
What is used to diagnose obstructive sleep apnea
Polysomnography
What are the complications of obstructive sleep apnea
Cor pulmonale
Poor growth
Poor school performance
What is cyanotic breath holding
Breath holding spells between the ages of one and three years old usually associated with temper tantrums or angry outbursts
It’s self-limited and very benign
What is Pallad Breath holding
Associated with fright
Patient becomes pale and hold breath
loses consciousness
What is the most commonly aspirated food
Peanuts
Popcorn, grapes, hot dogs are also common
What are the signs and symptoms of a foreign body aspiration
Cough, Strider, shortness of breath, cyanosis
Localized wheezing or new onset wheezing
How will a chest x-ray demonstrate foreign body aspiration
With an expiratory expiratory film. The effected side is the same appearance for both inspiration and expiration
Ball valve mechanism
What is the treatment for foreign body aspiration
Bronchoscopy
What is the pneumothorax
Intrapleural accumulation of air, maybe spontaneous or traumatic
What are the causes of the pneumothorax
CF, congenital lobar emphysema, asthma, pertussis,
Due to excessive cough
What is croup
Laryngotracheobronchitis
What are the most common causes of croup
Parainfluenza is the most common
Adenovirus, RSV, influenza
Most common three months to five years of age
What is the expected x-ray finding for croup
Staple sign
Suggestive of subglottic swelling