ENT

Question 1

Most common cause of congenital hearing loss?

What are syndromes associated with hearing loss?

Answer 1

Genetic (50%). Connexin gene mutation. Autosomal recessive.

ACKPSTTTW
Alport
CHARGE
Klippel-Feil
Pierre Robin
Stickler
Treacher Collin’s, trisomy 8, trisomy 21
Waardenburg

Question 2

What is considered abnormal hearing screen?

Answer 2

> 35 db abnormal -> amplification device

> 85 db severe -> Cochlear implants

Question 3

Difference in ABR and OAE

Answer 3

Types of loss: conductive, sensorineural, auditory dyssynchrony, central

ABR: automated brainstem response se. brainwave response to scalp electrode. Takes longer. Detects ALL TYPES. Less affected by outer and middle ear obstruction.

OAE: otoacoustic emissions. cochlear response. may miss sensorineural

Both: cut off 35 db, infants after 34 weeks. Both better at detecting mid to high frequency sounds compared to low frequency.