Cystic Fibrosis Flashcards
What is Cystic Fibrosis?
An inherited condition in which the lungs and digestive system become clogged with thick, sticky mucus
What causes Cystic Fibrosis?
Mutations in the CFTR gene
In which race is Cystic Fibrosis more common?
Caucasians
What characterises Cystic Fibrosis?
Chronic Bronchopulmonary infections and airway obstruction
What are the symptoms of Cystic Fibrosis?
Loose Oily Stools Failure to thrive Persistent Chest Infections Malnutrition Diabetes Sinusitis
A one year old child, caucasian with loose oily stools and failure to thrive presents. They have had persistent chest infections. Cause?
Cystic Fibrosis
Management of CF?
- Postural Drainage
- Nutritional Supplements
- Antibiotics for chest infections
- Bronchodilators for symptoms
Describe the use of physiotherapy in CF?
Postural drainage is done
This involves tipping the body upside down so the affected lobe is uppermost
Percussion helps loosen mucus
Describe the use of antibiotics in CF?
These are given for chest infections
Given EARLY on in HIGH DOSES for LONGER than normal
Describe the use of Bronchodilators in CF?
Salbutamol to relieve symptoms
Corticosteroids to reduce inflammation
Describe the use of nutrition in CF?
Pancreatic enzymes, vitamin and high calorie diet
How is CF diagnosed?
Sweat Test
Genetic Testing
