cystic fibrosis

Question 1

what systems are involved with CF

Answer 1

Nose, liver, gallbladder, bone, intestines, lungs, heart, spleen, stomach, pancrease, reproductive

all of them

Question 2

what are the common sugns and symptoms of CF

Answer 2

salty skin

chronic resp problems

lung infections

poor weight/weight loss

meconium ileus

bulk/gresy stool

Question 3

how is CF diagnosed

Answer 3

screen the baby - 48 hr via blood test

if this is positive then do the the

sweat test

Question 4

what is the sweat test looking at

Answer 4

how much chloride there is in your sweat

Question 5

what is the routine needed to manage CF

Answer 5

Nebulizer, quarterly testing, pulmonary function test, breathing tech, vest, chest percussion, exercise, diet

Question 6

nutrition and CF

Answer 6

Those with CF have poor absorption of nutrition and have increased cal burning

120-200% cal needs

Question 7

diet of those who have CF

Answer 7

high caloric, high protein, high salt

Question 8

CF supplements

Answer 8

pancreatic enzymes (food break down), vit supplements A, D, E, K

Question 9

G tubes and develpopment milestone

Answer 9

have to make sure this does not get in the way of them

Question 10

CF and DM

Answer 10

 Adulthood 1 and 3
 Therefore those who have CF are constantly monitored – screening starts at age 10

Question 11

reproduction

Answer 11

male and female have reduced fertility

males- block vas deferans

Question 12

FEV1 levels CF

Answer 12

when we are born they are somewhat normal and then they quick drop

Question 13

CF and exercise time

Answer 13

o Children – 60 mins per day
o Adults – 20-30 min a day

use the talk test to gage the intensity