Congenital Pulmonary Flashcards
Cystic Fibrosis is a genetic disease that causes a _________ transport disfunction.
ion
What protein is affected with CF?
CFTR - a gene that is involved in the production of sweat, mucus and digestive fluids
How does CF affect the lungs?
- results in thick mucus
- predisposes pt to bacterial infections
- pt develops obstructive lung disease
- pt gets loss of lung function
How does CF effect the gut?
- exocrine pancreatic insufficiency
- loss of bicarbonate rich pancreatic fluids
- reduced gut hydration
- loss of digestion
poor digestive function leads to:
- poor absorption
- chronic constipation
- distal intestinal obstruction syndrome
What is meconium ileus?
meconium: the 1st feces or stool of the newborn
ilieus: diminished or absent peristalsis
Cystic Fibrosis can not only effect the lungs and the gut but can also effect the __________, resulting in osteoporosis.
bone
Is pregnancy possible for women w CF?
yes
can men have children with other women if he has CF?
Most likely not
What test can we use to assess the chloride content in sweat?
sweat test
what drugs do we use for cystic fibrosis?
bronchodilators, mucolytics, decongestants, antibiotics
What pt ed. could we give pts w CF?
Take a vitamin supplement, eat calorie-dense meals, and drink a lot of fluids.
W/ cystic fibrosis, pts practice ______ hygiene.
chest
Pulmonary edema occurs when:
the pulmonary IS fills with fluid that has leaded from the vasculature into the IS spaces
With pulmonary edema, it will move in to the alveoli spaces and ____________ alveolar surfaces.
decrease
What condition characterizes the phrase “I feel like I am breathing through water.”
Pulmonary edema
What are the 4 reasons pulmonary edema could be a result of?
a fluid overload
decreased serum albumin levels
lymphatic obstructions
increased capillary permeability
What 3 things characterizes the early stages of pulmonary edema?
a persistent cough
dyspnea (hypoxia)
intolerance to exercise
Trx of pulmonary edema is aimed at:
- maintaining MAP
- Improving oxygenation
- reduce fluids
is pulmonary edema a medical emergency?
yes