Congenital PH Flashcards

1
Q

Histo

A
  • Intimal thickening
  • Medial hypertrophy
  • Plexiform lesions
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
2
Q

C/s

A

o Exercise intolerance, tachypnea, syncope
o R CHF symptoms

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
3
Q

PE

A

o Loud/split S2
o Diastolic murmur from PI
o Holosystolic murmur from TR

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
4
Q

ECG

A
  • R axis deviation
  • Tall/peaked P wave
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
5
Q

CTX

A
  • Enlarged MPA
  • Tortuous PAs
  • Pulmonary infiltrates
  • R sided cardiomegaly
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
6
Q

Echo

A
  • ↑ R side: RVH/RVE/RAE
  • PA systolic pressure estimation with TR jet velocity
  • PA diastolic pressure estimation with PI jet velocity
  • Other signs of PH: RPA motion, ↓ AT and AT/ET ratio
  • Reduced L side parameters
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
7
Q

Cardiac KT pressure study

A

accurate evaluation of PAP and PVR

How well did you know this?
1
Not at all
2
3
4
5
Perfectly