Congenital Chest Wall Anomalies Flashcards
Are congenital deformities of the ribs common or uncommon and important or unimportant
Common and unimportant
Complication of absence of one or more ribs
Lung hernia
paradoxical movement of affected part of the chest
Which type of rib is more at risk of having an extra number
Cervical ribs
Syndrome caused by extra cervical rib
Thoracic outlet syndrome
What is thoracic outlet syndrome
Cervical cervical rib compressing nearby nerves and arteries causing Shoulder and neck pain (c7T1)
Is the total absence of sternum rare or common
Very rare
Complication of total absence of sternum
Ectopia cordis which carries high mortality
Where can you find Partial defects presents in the sternum
In the upper sternum
lower sternum
Best period To perform a correction of upper sternum defects
Neonatal period
What is pectus excavatum
Normal manubrium with depressed Gladiolus in the thorax
Attached lower costal cartilages are acutely angulated
What is the main consequence/complication of pectus excavatum
Cosmetic or psychological trauma to the child
Main investigation in pectus excavatum
Lateral chest x-ray
Treatment of Pectus excavatum
Conservative with braces
Surgical correction around 8yo with steel bar which is removed 6-8 weeks after
Which type of patient is eligible for vacuum bell in pectus excavatum
Patient with mild pectus excavatum
What is Pectus carinatum
Sternum is pushed forward and the ribs are flattened laterally
Why is surgical correction hardly if ever required in pectus carinatum
Because it rarely causes symptoms
What is the main way to correct pectus carinatum
Braces with dynamic compression
Are there indication for surgery in Pectus carinatum
More than 10 psi in pressure
Open perichondrium
Resect protruding cartilage
Partial osteotomy to push down part of protruding sternum
What are the 3 components of Poland syndrome
Congenital malformation of chest wall
Ipsilateral pectoralis major defect
Ipsilateral limbs abnormalities