CLIPP 26: 9-week old male not gaining weight

Question 1

By when should infants have doubled their birth weight?

Answer 1

4 months

Question 2

Why is decreased velocity of growth of head circumference concerning?

Answer 2

Brain growth is reflected in head circumference

Question 3

How many calories per day should infants consume during the first 4 months of life for proper growth?

Answer 3

100-110

Question 4

Sweat chloride > 60mg/dL is consistent with..?

Answer 4

cystic fibrosis

Question 5

Two metabolic disorders that may cause a false positive sweat chloride test?

Answer 5

False positives can occur with a number of metabolic disorders including adrenal insufficiency and hypothyroidism.

Question 6

Inheritance pattern of CF?

Answer 6

autosomal recessive

Question 7

Three-pronged approach to CF treatment?

Answer 7

Nutritional management, with enzymes and vitamins and extra calories
Airway clearance, and
Treatment of airway infections.

Question 8

GU abnormality associated with CF?

Answer 8

Agenesis of vas deferns

Question 9

Is CF included in the newborn screen?

Answer 9

Yes