clinical neurology soal 131-160 Flashcards
Stage 2 sleep is characterized by A. K complexes B. delta waves C. desynchronization of the EEG D. REM sleep E. somnambulism
A. K complexes
V&A p. 405. Delta waves are prevalent in stage 3 and 4 sleep. Desynchronizationof the EEG occurs in REM sleep, and somnambulism occurs almostexclusively i l stage 4 sleep.
The protein dystrophin is absent. A. Becker's muscular dystrophy B. Duchenne's muscular dystrophy C. Emery-Dreifuss muscular dystrophy D. Landouzy-Dejerine (fascioscapulohumera1) dystrophy E. myotonic dystrophy
B. Duchenne’s muscular dystrophy
The protein dystrophin is structurally abnormal.
A. Becker’s muscular dystrophy
B. Duchenne’s muscular dystrophy
C. Emery-Dreifuss muscular dystrophy
D. Landouzy-Dejerine (fascioscapulohumera1) dystrophy
E. myotonic dystrophy
A. Becker’s muscular dystrophy
the most common adult form of muscular dystrophy
A. Becker’s muscular dystrophy
B. Duchenne’s muscular dystrophy
C. Emery-Dreifuss muscular dystrophy
D. Landouzy-Dejerine (fascioscapulohumera1) dystrophy
E. myotonic dystrophy
E. myotonic dystrophy
Prominent pseudohypertrophy of the calves is seen in Becker and in this type
A. Becker’s muscular dystrophy
B. Duchenne’s muscular dystrophy
C. Emery-Dreifuss muscular dystrophy
D. Landouzy-Dejerine (fascioscapulohumera1) dystrophy
E. myotonic dystrophy
B.Duchenne’s muscular dystrophy
Contractures of the elbow flexors and neck extensors occur early
A. Becker’s muscular dystrophy
B. Duchenne’s muscular dystrophy
C. Emery-Dreifuss muscular dystrophy
D. Landouzy-Dejerine (fascioscapulohumera1) dystrophy
E. myotonic dystrophy
C. Emery-Dreifuss muscular dystrophy
Abnormal gene is on chromosome 4 A. Becker's muscular dystrophy B. Duchenne's muscular dystrophy C. Emery-Dreifuss muscular dystrophy D. Landouzy-Dejerine (fascioscapulohumera1) dystrophy E. myotonic dystrophy
D. Landouzy-Dejerine (fascioscapulohumera1) dystrophy
Lens opacities are found in 90% of patients
A. Becker’s muscular dystrophy
B. Duchenne’s muscular dystrophy
C. Emery-Dreifuss muscular dystrophy
D. Landouzy-Dejerine (fascioscapulohumera1) dystrophy
E. myotonic dystrophy
E. myotonic dystrophy
occasionally associated with congenital absence of an involved muscle
A. Becker’s muscular dystrophy
B. Duchenne’s muscular dystrophy
C. Emery-Dreifuss muscular dystrophy
D. Landouzy-Dejerine (fascioscapulohumera1) dystrophy
E. myotonic dystrophy
D. Landouzy-Dejerine (fascioscapulohumera1) dystrophy
Masseter atrophy, ptosis, and frontal baldness are characteristic.
A. Becker’s muscular dystrophy
B. Duchenne’s muscular dystrophy
C. Emery-Dreifuss muscular dystrophy
D. Landouzy-Dejerine (fascioscapulohumera1) dystrophy
E. myotonic dystrophy
E. myotonic dystrophy
Abnormal gene is on chromosome 19. A. Becker's muscular dystrophy B. Duchenne's muscular dystrophy C. Emery-Dreifuss muscular dystrophy D. Landouzy-Dejerine (fascioscapulohumera1) dystrophy E. myotonic dystrophy
E. myotonic dystrophy
For questions 132-141 see V&A pp. 1494-1500, 1503-1504. Duchenne andBecker muscular dystrophies are X-linked recessive disorders characterized bythe absence of the gene product dytrophin in the former and the presence of astructurally abnormal form of the product in the latter. Weakness and pseudohypertrophyof certain muscles (notably the calf) occur. The onset is later andthe course more benign in the Becker type. Myotonic dystrophy is the mostcommon adult form of muscular dystrophy and is characterized by an autosomaldominant inheritance, with the defective gene localized to chromosome 19q.Features include dystrophic changes in nonmuscular tissues (e.g., lens opacities)and a characteristic facies. Landouzy-Dejerine dystrophy is usually transmittedby autosomal dominant inheritance, and the abnormal gene has been localizedto chromosome 4. Congenital absence of a pectoral, brachioradialis, or bicepsfemoris muscle occasionally occurs. Characteristics of Emery-Dreifuss dystrophy,a benign X-linked dystrophy, include contractures of the elbow flexors,neck extensors, and posterior calf muscles.
Monoplegia without muscular atrophy is most often secondary to a lesion in the A. brainstem B. cortex C. internal capsule D. peripheral nerve E. spinal cord
B. cortex
The transmissable agent of Creutzfeldt-Jakob disease is inactivated by I. formalin II. autoclaving at 132°C under pressure for 1 hour III. alcohol IV. immersion for 1 hour in bleach A. I, II,III B. I. III C II, IV D. IV E. all of the above
C. autoclaving at 132°C under pressure for 1 hour, immersion for 1 hour in bleach
The most common finding on audiography in patients with acoustic neuromas is A. flat loss B. high-frequency loss C. low tone loss D. normal audiogram E. trough-shaped loss
B. high-frequency loss
Median sensory responses from the index and middle finger are low in amplitude,but motor conduction velocities of the hand muscles are normal. A. lateral cord lesion B. lower trunk lesion C medial cord lesion D. middle trunk lesion E. upper trunk lesion
D. middle trunk lesion