CF Flashcards

1
Q

pulmonary system

A

mature at age 20
aging bring less elasticity
takes muscles to breathe

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2
Q

Gas Exchange in the PS

A

right side of heart to the lungs to thel eft side of the heart (oxygrn rich blood goes into the body)

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3
Q

Lung inmune defense mechanisms

A

cillia filter out dust particles causes coughing then unwanted materials are swallowed and stomach acids takes care of them or coughed out

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4
Q

Effects of malnutrition of PS

A

adversly effects lung structure, elsticity and function, resp muscle mass, strentght and endurance,lung immune defense control of breahting

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5
Q

effects of pul disease on nutritional status

A

substantional increase energy needs requirments
wt loss is significant with a poor prognosis
the disease and treatments can mke adequate food intake and digesetion difficult

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6
Q

Pulse oximetry goal

A

95%-99% if below pt will feel weak

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7
Q

CF

A

autosomal recessive inherited disorder new meds and treatments not a death sentence anymore

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8
Q

CFTR mutations

A

impact transport of chloride sodium and bicarbonate
endocrine glands effected thick sticky mucus secreted

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9
Q

Merconium ileus

A

bodys 1st stool unable to pass it

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10
Q

CF treatments

A

antibiotics for resp infections
pancreatic enzymes for absoption
nutional support
mucous thinners
postural drainage
inhaled bronchodilators

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11
Q

CF goal BMI for kids

A

50th percentile or higher
below there isless air they have to psuh out

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12
Q

CF adult goal BMI

A

M 23 F 22

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13
Q

CF mnt

A

imporve nutrional status is closley associated with helathier lungs
prevention and ealry intervention are key

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14
Q

IMproving BMI

A

indivualize assesment and plan
maximize caloric intake
maximize absoption with enzymes
use nutional supplements
consider appetite simtulants

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15
Q

nocturnal feeds risk

A

wake up with full belly no breakfast impact daily intake

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16
Q

What we monitor with the intervention

A

stooling (with enzyme absoption)
labs ( nutional supplements)
appetite
growth

17
Q

COntributors to CF related inflamation

A

LAA and ALA

18
Q

Infants

A

give enzymes in applesauce bf feeding ( any age

19
Q

Cause of death top 3

A

lung complications trnasplant complications liver disease (10-15% pt)

20
Q

CF RD role

A

monitor asess growth weight
optimize BMI
pancreatic enzyme therapy
vit min supplemntation

21
Q

cor pulmonae

A

right side heart failure of the heart to the lungs