cardiomyopathy - restrictive

Question 1

Causes of restrictive cardiomyopathy (3)

Answer 1

-Granulomatous disease (sarcoidosis,amyloidodis)
-idiopathic
-post MI-fibrotic

Question 2

How common is restrictive cardiomyopathy

Answer 2

Rare

Question 3

Investigations to diagnose restrictive cardiomyopathy (3)

Answer 3

ECG
ECHO
cardiac catheterisation (diagnostic)

Question 4

Pathophysiology of restrictive cardiomyopathy (2)

Answer 4

Rigid fibrotic myocardium fills poorly and contracts poorly
=> decreased CO

Question 5

Symptoms of restrictive cardiomyopathy (5)

Answer 5

Severe:

-dyspnoea
-S3 + S4 sounds
-oedema
-congestive heart failure
-narrow pulse pressure (normally 120/80 but here it’s 105/95 and consequently blood stasis due to the decreased gradient)

Question 6

Treatment for restrictive cardiomyopathy (3)

Answer 6

None
Consider transplant
Patients typically die within 1yr