Cardiomyopathies

Question 1

Primary Cardiomyopathies

Answer 1

due to an idiopathic process effecting the myocardium

Question 2

Secondary Cardiomyopathies

Answer 2

related to a specific heart muscle disease

Question 3

Dilatated (Congestive, DCM, IDC)

Answer 3

ventricular enlargement and systolic dysfunction, from ischemic heart disease

Question 4

Hypertrophic (IHSS, HCM, HOCM)

Answer 4

inappropriate myocardial hypertrophyin the absence of HTN or aortic stenosis… diastolic dysfunction

Question 5

Restrictive (Infiltrative)

Answer 5

abnormal filling and diastolic function, think post radiation and amyloid cases

Question 6

IDC

Answer 6

a disease of unknown etiology that principally affects the myocardium
LV dilatation and systolic dysfunction

Question 7

Alcohol septal ablation (NSRT)

Answer 7

Controlled myocardial infarction of the basal ventricular septum to ↓ gradient.
First septal artery occluded with a balloon catheter and ETOH injected distally

Question 8

Restrictive CardiomyopathyDiagnosis

Answer 8

**CXR-signs of CHF without cardiomegaly
EKG-nonspecific changes most likely
ECHO-thickened LV walls with normal or slightly decreased volume

Question 9

Amyloid heart disease

Answer 9

Thickened, firm, rubbery ventricular muscle
Major diastolic dysfunction
Abnormal Q waves – look like an M.I.
Conduction disturbances, arrhythmias not uncommon
Echo: thickened walls everywhere