Cardiology-Notes Flashcards
What might a normal newborn EKG show?
physiologic R axis deviation
What is acrocyanosis? When is it normal?
peripheral cyanosis
from peripheral vasoconstriction
can be normal in newborns, but should resolve
if it persists–think about central cause-heart defect.
Cyanosis w/o respiratory distress–what should you think of?
congenital heart defect
How do congenital cyanotic heart disease patients react to 100% oxygen?
no improvement
How might polycythemia in a patient with congenital heart dx contribute to acrocyanosis?
increased RBCs (as a reaction to cyanosis) can cause sluggish blood flow & prompt peripheral cyanosis
What are some symptoms associated with a pathologic murmur in an infant?
diaphoresis
tiring with feeds
poor weight gain
What are some symptoms associated with a pathologic murmur in children?
chest pain dizziness syncope SOB fatigue
What are some concerning physical exam findings of a murmur?
holosystolic diastolic >=3/6 INCREASES with standing or Valsalva (decreased blood return) Loud, fixed split, or single S2 decreased or absent femoral pulses
What is the work up for a concerning murmur in a child?
CXR (cardiomegaly)
EKG (hypertrophY)
ECHO
cardio referral
Holosystolic harsh @ LLSB. Do you need an ECHO?
Yes, possibly a VSD.
What are the heart defects of R–>L shunts? Blue babies?
1-5
- Truncus Arteriosus (1 vessel)
- Transposition of the Great Vessels (2 vessels)
- Tricuspid Atresia (tri-3)
- Tetrology of Fallot (4-tetra)
- TAPVR (5 letters)
What are the heart defects of L–>R shunts? Blue kids?
1-3
1 VSD
2. ASD
3. PDA
Which congenital heart defects are associated with Digeorge 22q11?
the Ts
Truncus Arteriosus
Tetrology of Fallot
Which heart defect is associated with congenital rubella?
PDA
Ruby is the color of love. public displays of affection.
Which heart defects are associated with Turner’s syndrome?
coarctation of the aorta
bicuspid aortic valve
Which cardiac conditions are associated with marfan’s? & ehlers danlos?
aortic root dilation aka ascending thoracic aortic aneurysm
increased risk for aortic dissection
MVP
aortic insufficiency (regurg)
Diabetic moms have increased risk of children with what?
transposition of the great vessels.
Friedrich’s ataxia is associated with what?
hypertrophic cardiomyopathy
What are the features that are shared by Marfan syndrome and homocystinuria?
pectus deformity tall stature with high arm/height ratio larger lower segment than upper segment arachnodactyly joint hyperlaxity skin hyperelasticity scoliosis
What are the features of Marfan syndrome that distinguish it from homocystinuria?
autosomal dominant
normal intellect
lens dislocation
aortic root dilation
What are the features of homocystinuria that distinguish it from Marfan’s syndrome?
autosomal recessive intellectual disability thrombosis megaloblastic anemia fair complexion
When can PDA be beneficial? What is it associated with? What does the murmur sound like?
beneficial in R–>L shunts blue babies
associated w/ congenital rubella
sounds like a continuous machine like murmur
What is the presentation of PDA?
may be asymptomatic accentuated increased pulses if large-can get CHF tachypnea, tachycardia, poor feeding, FTT can lead to Eisenmenger
WHat is the workup and treatment of a PDA?
dx: via ECHO
treatment: usu closes in a few weeks
can ligate surgically if it doesn’t close or use indomethacin
keep it if they have R–>L shunt.