Cardiology Flashcards
What are the 5 types of cyanotic heart defects?
Truncus
Transposition of the Great Vessels
Tricuspid Atresia
Tetrology of Fallot
Total Anomalous Pulmonary Venous Return (Obstructive)
What 4 anomalies constitute Tetralogy of Fallot? What prenatal factors are associated with it?
Aortic Override
VSD
RVH
Right Ventricular outflow obstruction
Maternal rubella or viral illness
Kids with TOF will often squat after exercise - why?
Causes trapping of desaturated blood in the LE and Increaces SVR while the RV outflow is fixed
- Dec, R to L shunt
- Inc. pulmonary blood flow
- Inc arterial saturation
Tet Spell
Kids with TOF suddenly develop cyanosis
Inc. CO w/ fixed RV outflow - Increased R to L shunt
What are 3 things on CXR that can help diagnose Tetrology of Fallot?
Boot shaped heart
Decreased pulmonary vascular markings
Right aortic arch (25%)
What is the most common cyanotic congenital heart defect presenting in the neonatal period?
Transposition of the Great Vessels
*Must have ASD &/or VSD for mixing*
What does this patient have? How do you treat it?
Transposition of the Great Arteries w/ Intact Ventricular septum
*Need PGE1 for patent PDA & Early Balloon Atrial Septostomy
**Arterial Switch is definitive**
Subendocardial cushion defects are associated with what genetic syndrome? What defects are typically seen?
Trisomy 21
*Ostium primum ASD
*VSD
What are signs/symptoms of ASDs? (2)
Wide, fixed split S2
CHF & pulmonary HTN in 20s-30s
What size ASD are likely close on their own? Which are unlikely?
90% close spontaneously
< 3mm = 100%
> 8mm = unlikely
What is the most common congenital heart disorder?
VSD (membranous)
What percent of VSDs spontaneously close? When is intervention indicated? How do you treat?
30-50%
CHF, pulmonary HTN, growth failure
Diuretics and digitalis
Surgery
What is the main cause of PDA closure?
Ductal PO2 > 50 mmHg
Eisenmenger’s Syndrome
An unrepaired left-to-right shunt turns into a cyanotic right-to-left shunt
Increased pressure leads to pulmonary HTN
An opening snap wth a presystolic murmur is indicative of what?
Mitral Stenosis
Sequela of acute rhematic fever
Supravalvular aortic stenosis is associated with __________.
Idiopathic Hypercalcemia
Midsystolic click and late systolic murmur
Mitral Valve Prolapse
*nearly all Marfan’s pts have it*
Symptomatic treatment: β-blocker for chest pain
Coarctation of the Aorta is seen in 1/3 of patients with ____________.
Turner’s Syndrome
Pulmonary flow murmurs, physiologic pulmonary branch stenosis and Still’s murmurs can all be heard best when the patient is _______.
Supine
All are innocent
Common to all innocent murmurs (5)
Absence of structural defects
Normal S1/S2
Normal peripheral pulses
Normal CXR and ECG
Asymptomatic
**Usually systolic and < Grade III