AMBOSS

Question 1

adult-onset asthma, chronic sinusitis, mononeuritis multiplex (foot drop, loss of sensation in the distribution of the ulnar nerve), subcutaneous skin nodules, and palpable purpura

Answer 1

eosinophilia with granulomatosis/Churg-Strauss

Question 2

differentiate XLA from THI

Answer 2

B cells are decreased in XLA

Question 3

organisms that cause recurrent problems in XLA

Answer 3

s pneumo
h flu
n meningitids

Question 4

linear deposition of IgG along the glomerular basement membrane

Answer 4

goodpastures

Question 5

recurrent pyogenic upper respiratory infections associated with chronic diarrhea due to giardiasis

Answer 5

IgA deficiency

Question 6

absence of C4d staining in a transplanted kidney

Answer 6

host T cells attacking the graft

Question 7

other disorder that has an absent thymic shadow

Answer 7

SCID (adenosine deaminase deficiency)

Question 8

PCP in a 5 month old with silver stain in lungs

Answer 8

CD40 ligand