(5) Resp Management in Neuromuscular Disease Flashcards
What is Motor Neuron Disease (MND)?
progressive neuro condition that attacks the motor neurones or nerves in the brain or sc meaning messages sto reaching the muscles
What 3 major sites are damaged in a degenerative neurological condition?
- Anterior horn cell (LMN symptoms)
- Corticospinal tract (UMN symptoms)
- Motor nuclei in brain stem (bulbar palsy)
What are UMN signs (3)?
- weakness
- spasticity
- brisk reflexes
What are LMN signs (5)?
- weakness
- muscle wasting
- fasciculations
- cramping
- decreased reflexes
What are bulbar signs (6)?
- dysphagia
- slurred/loss speech
- breathing difficulty
- weak cough
- problems managing saliva
- aspiration
What are 4 types of MND?
- Amyotrophic Lateral Sclerosis (ALS)
- Progressive Bulbar Palsy (PBP)
- Progressive Muscular Atrophy (PMA)
- Primary Lateral Sclerosis (PLS)
Where is the breathing rate controlled?
medulla oblongata (resp centre)
What are the muscles of ventilation?
- diaphragm (C3-5)
- intercostals (T1-11)
- Abdominals (T5-12)
- Accessory Muscles
What are the inspiratory muscles responsible for?
ventilation
What are the expiratory muscles responsible for?
coughing
What are the bulbar muscles responsible for?
protecting the airway
What are the factors in restrictive lung disease?
_ total lung volume too low
- stiffness in chest wall
- reduced FVC
What are the factors in obstructive lung disease?
- difficulty exhaling air from lungs
- smaller airways partially blocked
- results decreased FEV1 & FEV1/FVC ratio
What are different types of resp complications?
- paradoxical breathing patterns
- underdeveloped lungs
- hypercapnia
- weak/ineffective cough
- recurrent RTI
- sleep disordered breathing
What causes respiratory failure in MND (5)?
- resp muscle weakness
- reduced chest compliance
- increased resistive load
- upper airway muscle weakness
- impaired control of breathing