Week 7.2 Pediatric Candidacy Flashcards

1
Q

when did the FDA 1st approve CI’s for children

A

june 1990

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2
Q

AB audiometric threshold requirements for children

A

severe to profound bilateral sensorineural hearing loss (>70 dB HL)

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3
Q

AB auditory skills and speech recognition in younger children

A

<4 years of age: failure to reah developmentally appropriate auditory milestones (such as spontaneous response to name in quiet or to environmental sounds) measured using the infant-toddler meaningful auditory integration scale or meaningful auditory integration scale; or <20% correct on a simple open-set word recognition test (multisyllabic lexical neighborhood test (MLNT)) administered using monitored live voice (70 dB SPL)

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4
Q

AB auditory skills and speech recognition in older children

A

> 4 years of age: <12% on a difficult open-set word recognition (phonetically balanced kindergarten test) or <30% on an open-set sentences (hearing in noise test for children) administered using recorded materials in the sound field (70 dB SPL)

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5
Q

AB amplification requirements for children

A

use of appropriately fitted hearing aids for at least 6 months in children 2-17 years, or at least 3 months in children 12-23 months of age. The minimum duration of hearing aid use is waived in the presence of ossification concerns

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6
Q

cochlear audiometric threshold requirements in children

A
  • 12-23 months: bilateral profound SNHL

* 24 months-18yrs: bilateral severe-to-profound SNHL

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7
Q

Cochlear auditory skills and speech recognition in younger children

A

lack of progress in the development of simple auditory skills as quantified an a measure such as the Meaningful Auditory Integration Scale or the Early Speech Perception test

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8
Q

cochlear auditory skills and speech recognition in older children

A

= 30% correct on MLNT or lexical neighborhood test (LNT), depending on the child’s cognitive and linguistic skills

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9
Q

cochlear amplification requirements for children

A

use of appropriate amplification and participation in intensive aural habilitation over a 3 to 6 month period

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10
Q

med-el audiometric threshold requirements

A

profound bilateral SNHL with thresholds of 90 dB HL or greater at 1000 Hz

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11
Q

med-el auditory skills and speech recognition in younger children

A

lack of progress in the development of simple auditory skills in conjunction with appropriate amplification

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12
Q

med-el auditory skills and speech recognition in older children

A

<20% correct on the MLNT or LNT depending on cognitive ability and linguistic skills

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13
Q

Mel-el amplification requirements for children

A

use of appropriate amplification and participation in intensive aural habilitation over a 3 to 6 month perios
*radiologic evidence of cochlear ossification may justify a shorter trial with amplification

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14
Q

when can you use conditioned play audiometry

A

24-30 months up to 6 yrs

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15
Q

CI criteria for children (audiometric thresholds)

A
  • 12-24 months: bilateral profound SNHL
  • > 24 months
  • –cochlear= bilateral severe to profound SNHL
  • –AB and Mel-el= bilateral profound SNHL
  • can implant earlier then 12 months by decision of the CI team
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16
Q

different ways to assess hearing status of children

A
  • objective testing
  • –case history
  • –tymps
  • –acoustic reflex
  • –OAE
  • –ABR
  • –EcochG (will tell you pre synaptic or post synaptic lesion)
  • speech recognition testing
  • accurate diagnosis (VRA or play audiometry is really helpful to know what is really going on, this is preferable)
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17
Q

when to use evoked potential testing for candadicy for children

A
  • use on your itty bittys who cant give behavioral responses

* can also use to try and find the site of lesion

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18
Q

about what percent of children with HL have auditory neuropathy and what is the significance of this

A
  • about 9% of kids with HL have AN
  • this is important to know because it would affect the recommendations depending on type 1 or type 2
  • –type 2 is more of damage to the synapse of the IHC
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19
Q

hearing aids eval in CI candidate for children

A
  • testing conditions: the best-aided condition
  • HA verification process
  • –PMM or test box verification with pt specific real ear to coupler difference (RECD) corrections
  • –DSL m[i/o] should be used
  • –verify target at speech-input levels corresponsing to soft, average, and loud, such as 50, 60, and 70 dB SPL
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20
Q

speech recognition testing for children basic

materials and presentation level

A
  • speech testing material
  • –recorded is necessary for older children
  • –some children only respond to MLV, but really need to do recorded
  • —–use the multisyllabic lexical neighborhood test (MLNT) and monosyllabic lexical neighborhood test (LNT)- both are recorded
  • presentation level
  • –use 60 dB A
  • amplification trial period
  • –importance
  • –6 months
  • –shorter trial
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21
Q

speech recognition testing in younger children

A
  • mainly looking at auditory skills development via questionnaires
  • closed set tests are recommended for younger kiddos
  • –Nu-chips
  • –WIPI
  • –CRISP Jr
22
Q

NU-CHIPS

A

northwestern university children’s perception of speech

  • picture booklet with 4 pics per page (25% chance)
  • vocab level is 2.5-5 years
23
Q

WIPI

A

word identification picture intelligibility

  • picture booklet with 6 pictures per page (16.7% chance)
  • vocab level is 3-5 years
24
Q

CRISP Jr

A

children’s realistic intelligibility of speech perception (computer based)

  • 16 words that are body parts or names of objects
  • age group is 2.5-5 years
25
FDA speech recognition testing in older children in order of developmentally appropriate progression
* early speech perception (ESP) test * multisyllabic lexical neighborhood test (MLNT) * lexical neighborhood test (LNT) * phonetically balanced kindergarten (PBK) word recognition test * BabyBio sentences for children * CRISP (childrens realistic intelligibility of speech perception (computer based)
26
ESP
early speech perception test * closed-set (36 words, 3 lists) * ages 2-6 years
27
MLNT
multisyllabic lexical neighborhood test * open-set, 2 lists of 12 lexically easy and 2 lists of 12 hard mutisyllabic words (level 3-5 years) * words and phonemes correct
28
LNT
lexical neighborhood test | *2 lists of 25 lexically easy and 2 lists of 25 hard monosyllabic words (level 3-5 years)
29
PBK test
phonetically balance kindergarten word recognition test * minimum 4 years * ope-set, 50 words-phonemes and word correct
30
BabyBio sentences for children
* at least 5 years old | * 16 lists, each has 20 lists of 3-12 words
31
CRISP
children's realistic intelligibility of speech perception (computer based) * 25 spondees * age group is 4-7 years
32
FDA labeled ped CI candidacy for speech for AB
* young=<20% on MLNT | * older= <12% on open set (PBK) or <30% on HINT-C
33
FDA labeled ped CI candidacy for speech for cochlear
* young= lack of progress | * older=<30% on MLNT or LNT
34
FDA labeled ped CI candidacy for speech for med-el
* young= lack of progress | * older=<20% on MLNT or LNT
35
evaluating progress of auditory skill for kids 0-3 years
* looking to see auditory skills and progress during the HA trial * must be done via parental history and validated questionnaires: - --infant-toddler version of the Meaningful Auditory Integration Scale (IT-MAiS) - -----0-3 yrs - -----10 item parental interview - -----open-ended questions with scores ranging from 0 (never) to 4 (always) - --the LittlEars Questionnaire - -----0-24 months in normals (or up to 24 months following implantation) - -----35 yes/no questions - -----questions are hierarchical, so ceiling at 6 consecutive no answers - --the auditory skills checklist (ASC) - ------0-3 yrs - -----parental interview style with 35 items assessing detection, discrimination, identification, and comprehension - -----soreing 0= child does not have the skill; 1= child has skill developing; 2= child demonstrated the skill - --functioning after pediatric cochlear implantation (FAPCI) questionnaire - -----2-5 yrs - -----23 items does not require parental interview - -----provides baseline (pre-op) - --functional auditory performance indicators (FAPI) - -----assess sound awareness, meaningful sounds, auditory feedback,sound localization, discrimination, short-term auditory memory and linguistic auditory processing - -----scoring: emerging (0-35%); in process (36-79%); acquired (80-100%) - --3mo until all acquired - --early language milestone scale (ELM) - -----0-3 yrs - -----43 items designed to assess language development (expressive, receptive,a and visual language--parental interview
36
evaluating progress of auditory skills for preschool to school-age children
* common questionnaires - --the meaningful auditory integration scale (MAIS) - -----3-5 yrs - -----10 item parental interview style questionnaire - --the parents' evaluation of aural/oral performance in children (PEACH) - -----3-7 yrs - -----13 items designed for parental completion - -----parent reflect on the child's listening behavior over the previous week and assigns a numerical value ranging from 0 (never) to 4 (always)
37
SLP's role in CI
* critical role in CI candidate selection | * at least SLP eval during candidacy selection process should take place during the HA trial (after verification)
38
social worker and physiologist involvement in CI candidate selection
* often helpful for families struggling with the diagnosis * help to determine family dynamics and level of dedication to the recommended post-op therapy schedule * social workers can provide counseling and support in financial options
39
medical and surgical issues with ped CI candidacy
* medical team ensures that candidates are current on recommended immunizations * a pre-op medical eval anesthesia) and other medical specialties as needed * imaging: CT and MRI
40
vestibular considerations for ped CI candidacy
* vestib impairment is the single most common associated feature of SNHL - --many pts with HL experience dizziness and/or imbalance * balance system: detection and integration from the visual, proprioceptive, and vestib system - --vestib system is at the biggest risk during cochlear implantation * 5 vestibular end organs within each ear: - --3 SSC that detect and encode angular accelerations - -----info detected here triggers the vestibulo-ocular reflex, leading to maintenance of stable vision during movement - -----2 remaining= otolith (utricle and saccule)- linear movements such as gravity and head tilts - ---------important for postural stability through vestibulo-colic and vestibulo-spinal reflexes - ---------important for gross motor skill development (learning to sit, stand, and walk)
41
vestibular function and HL
* 72% of children and adults with significant SNHL have some level of vestib dysfunction-type depends on underlying inner ear pathology - --for cases evaled for CI, up to 50% have SCC abnormalities, and up to 44% have abnormal otolith function * genetic: - --Usher syndrome (Type I) - --pendred syndrome - --waardensburg syndrome - --cogan syndrome - --brachio-oto-renal syndrome - --CHARGE - --connexin 26 - --inner ear malformations - --enlarged vestibular aqueduct - --charcot-marie-tooth disease * Acquired: - --prematurity - --anoxia - --fetal alcohol syndrome - --meningitis - --CMV - --ototoxicity - --aging - --menieres - --labyrinthitis - --autoimmune inner ear disease - --trauma
42
pediatric vestibular considerations
* children with severe to profound HL are likely to demonstrate additional vestibular impairment * children with congenital SNHL demonstrate semicircular canal (41%) and otolith (42%) dysfunction * vestibular function in children is commonly overloooked. but congenital and early-onset vestib dysfunction may lead to significant delays in motor skill development * developmental milestones (upper limit) - --response to tilt (>36 months)-should right within seconds - --head control- 4 months - --sitting unsupported-9 months - --walk 18 months * motor function (standing on one leg) - --2.5 yrs= 1 sec - --3 yrs= 2 sec - --4 yrs=5 sec - -->/= 5 yrs= 8 sec (eyes open), 4 sec (eyes closed)
43
when to refer kid for vestib eval
* delayed motor development * delayed walking * loss of postural control= falls * episodes where pallor/vomiting * investigating etiology of HL +/- balance symptoms
44
barriers to ped CI
* lack of pt awareness * finances - --SEC - --insurance * lack of professional knowledge * lack of referrals
45
infants under 12 months and CI
* FDA candidacy is 12 months * no greater anesthetic risks for infants <12 months * surgical issues: - --intraoperative blood loss - --facial nerve damage - --skull thickness - --fixation of the internal device - --thin skin flap - --skull growth causing migration
46
SSD and amplification options
* CROS * osseointegrated bone conduction hearing device * remote mic system * CI - --improve speech in quiet and noise - --better spatial hearing - --tinnitus suppression in unilateral hearing loss
47
SSD in peds
* cochlear nerve deficiency: as many as 50% of children with SSD have cochlear nerve deficiency- CRUCIAL to get an MRI - --likely to reject CI * CMV-most common environmental cause of genetic HL - --some children with SSD due to CMV will make limited progress with implant due to cognitive/neural deficits associated with CMV * bacterial meningitis-if ossification has occurred, unlikely that a CI will be possible * enlarged vestibular aqueduct- relatively common cause of SSD; highly successful with Ci if duration of deafness prior to implantation is short
48
SSD in adults
* menieres - -CI with simultaneous labyrinthectomy (if vertigo) is generally successful * more successful if implanted after a short period of deafness (shorter the better) * adults should be highly motivated to be implanted
49
children with global developmental delay and CI
* no professional consensus on whether children with compromised cognition/severe global developmental delay should be implanted * difficulty in obtaining reliable behavioral estimated of hearing * expectations need to be managed with counseling
50
neurofibromatosis Type 2 | and CI
* autosomal dominant disorder * outcomes from cochlear implantation is variable but generally better than patients with an ABI * patient counseling * ***i think this really meant they do better with ABI