Vascular ectasias

Question 1

what are vascular ectasias?

Answer 1

a group of conditions characterized by localized dilation of pre-existing vessels

Question 2

name 5 vascular ectasias?

Answer 2

1. telangiectasia
2. nevus flammeus
3. struge-weber syndrome
4. spider angioma
5. Osler-Weber-Rendu disease

Question 3

what is telangiectasia?

Answer 3

dilation of preformed vessels creating a focal red pinpoint lesions on skin or mucous membranes

Question 4

what is nevus flammeus?

how does it look on histology?

what is a variant of nevus flammeus?

Answer 4

its the most common vascular ectasia, a pink to blue flat lesion on head or neck

you see dilation of dermal vessels that will regress

port wine stain because it does not regress

Question 5

what is sturge weber syndrome?

what symptoms are seen?

Answer 5

it is a ipsilateral CNS vascular malformation where you see Arterio-venous malformations in the leptomeninges that calcify and bleed

mental retardation, seizure

Question 6

what is a spider angioma?

this condition is associated with what disease?

Answer 6

arterio-venous malformation with a red dot in the center with reddish extensions (veins) radiating outward

hyperestrinism (increased estrogen) in preganancy and cirrhosis

Question 7

what is osler-weber rendu disease?

what symptoms do you see?

what is the presentation?

Answer 7

most common genetic vascular disease, autosomal dominant

dilated vessels on skin and mouth/GI

nose bleed, blood in vomit, GI bleed because vessels erode and rupture (lead to anemia)

Question 8

what is this?

Answer 8

sturge-weber syndrome

Question 9

what is this?

Answer 9

spider angioma

Question 10

what is this?

Answer 10

osler-weber-rendu