RVOT, LVOT, & Aortic Arch Anomalies Flashcards
Subvalvular obstruction involves hypertrophy of the ____ and usually occurs alongside other defects.
Infundibulum
____ obstruction may be in the form of a bicuspid pulmonary valve with varying degrees of pulmonary valve stenosis or atresia.
Valvular
Obstruction above the valve is usually in the form of ____ stenoses of the branch pulmonary arteries.
Discrete
There are two major forms of pulmonary valve stenosis:
- Fusion of the raphe, often with a bi-leaflet pulmonary valve which domes
- Severely thickened valve tissue with a tri-leaflet valve
____ will usually develop if RVOT obstruction is present.
RVH
The degree of RVH is dependent upon the amount of ____.
Obstruction
Most infants with an RVOT obstructions are ____.
Asymptomatic
Since the RV is not built to withstand high ____, early surgical intervention is necessary to reduce the stress on the RV.
Pressure
If there is a moderate to severe stenosis of the RVOT, they will have a loud ____ murmur.
Systolic
Pulmonary ____ is the complete obstruction of the RVOT with an atretic pulmonary valve.
Atresia
With pulmonary atresia, infants have no pulmonary blood flow except what is provided by the ____.
PDA
What are the two types of pulmonary atresia?
- Those with an intact IVS
- Those with a large VSD
Pulmonary atresia with intact IVS (PAIVS):
- Associated with a poor ____.
- Since there was not any blood exiting the RV during fetal development, the TV may be either severely ____ or ____.
- The RV is often ____ because of the lack of circulation in utero so it’s growth is restricted
- The RV will usually contract ____.
- Prognosis
- Stenotic/atretic; insufficient
- Hypoplastic
- Minimally
Pulmonary Atresia with Intact IVS:
- The smaller the RV and the more hypoplastic the TV, the poorer the ____
- There is a PFO or ____ ASD with a right-to-left shunt present (Venous return passes through PFO to get to LA and LV)
- There must be a ____ to supply blood flow to the lungs
- Prognosis
- Secundum
- PDA
____ is given to keep PDA open.
Prostaglandin
Placement of a systemic-to-pulmonary artery ____ is the most common procedure for PAIVS.
Shunt
What are most helpful views for visualizing RVOT obstruction?
- PSAX view at aortic level
- PLAX view of the RV, RVIT, and RVOT
- Subcostal/Apical 4 view of the RV
What are the steps to assessing an RVOT obstruction on echo?
- Assess RV size, function, and hypertrophy
- Assess TV morphology and function
- Evaluate PDA
- Evaluate IVS
- Evaluate ASD
- Measure main PA and branches
An LVOT obstrcution is any lesion that impedes the forward flow of blood from the LV to the ____.
Aortic arch
What are the three main types of LVOT obstruction?
Subvalvular, Valvular (bicuspid or stenosis), and Supravalvular
The mildest form of aortic valve disease is the ____
Bicuspid valve
Speed with which bicuspid valve calcification occurs depends upon:
- Severity of initial obstruction
- Calcium metabolism/cholesterol levels
- Gender (males more frequently)