Pulmonary Fibrosis Flashcards
1
Q
What is idiopathic pulmonary fibrosis?
A
Idiopathic interstitial pneumonia
Inflammatory cells infiltrate and pulmonary fibrosis of unknown cause.
Commonest ILD
2
Q
Symptoms of IPF?
A
Dry cough Exertional dyspnoea Malaise Weight loss Arthralgia
3
Q
Signs of IPF?
A
CYAnosis
Finger clubbing
Fine end inspiratory crepitations
4
Q
Complications?
A
Respiratory failure
Increased risk fo lung cancer
5
Q
What tests in idiopathic pulmonary fibrosis?
A
Blood:
ABG, Raised CRP, raised immunoglobulins
Imgaing:
CXR:
Reduced ung volume, bilateral lower zone reticulo-nodular shadows, honeycomb lung.
Spirometry - restrictive, reduced transfer factor
Lung biopsy - Usual interstitial pneumonia
6
Q
Management for idiopathic pulmonary fibrosis?
A
Supportive care: O2 Pulmonary rehabilitation Opiates Paliative care input
Lung transplant
Do not use high dose steroids
Nintedanib - immunosuppressant
