primary sclerosing cholangitis Flashcards
1
Q
what is it?
A
Biliary disease characterised by inflammation + fibrosis of intra and extrahepatic bile ducts
2
Q
what % of PSC have UC?
What else is it associated with?
A
80%
Crohns and HIV
3
Q
FEATURES?
A
pruritis (itching)
RUQ pain
4
Q
what is the Dx test?
A
ERCP
5
Q
associated with what antibody ?
A
ANCA +ve
6
Q
what does liver biopsy show?
A
onion skinning
obliterative cholangitis
7
Q
what is the Tx?
A
liver transplant
