peds deck 9 Flashcards
cerebral palsy is a disorder of _____________ & ______________
motor ability; muscle tone.
80% of cases of CP are _________________; while 6% come from ____________, and can also be acquired after neurologic injury, most commonly from ______________
prenatally acquired; hypoxic injury at birth; meningitis
anesthesia implications for pt with cerebral palsy
- can be spastic –> difficulty with positioning 2. poor muscle tone (consider diaphragm and heart) 3. poor vascular tone 4. poor temperature regulation 5. commonly have seizures/epilepsy - AVOID MEPERIDINE 6. scoliosis common
anesthesia considerations for the pt with Autism spectrum d/o
- be careful of preoperative medications 2. discuss preop medications/distraction techniques with caregivers (i.e. find out what works for the child)
anesthesia considerations for the pt with epilsepsy
- consider their at home medications 2. careful with preop medications 3. want them to take seizure meds DOS 4. metabolize medications (may need to redose NMBA more frequently) 5. NO MEPERIDINE
there are _________ types of spinal muscular atrophy and are classified by _____________
5; onset of sx
why do pts with spinal muscular atrophy commonly present for surgery?
- G-tubes 2. eventually need trach and become vent depedent
T/F: pts with spinal muscular atrophy are NOT neurologically intact
FALSE
pt presents for surgery and has Duchenne’s MD, what is the risk you should be concerned about
MD, specifically Duchennes can trigger MH crisis; plan for non-triggering anesthetic
pt comes in with Muscular dystrophy, but does not know they type, and it is not indicated in the chart, what should you plan for?
non-triggering anesthetic
how would you do a non-triggering anesthetic for the pt at risk for MH? (duchennes MD)
- flush machine according to manufacturers recommendation 2. utilize charcoal filters 3. ensure no succinylcholine is out 4. tape volatile agents
_______________ is the absence of parasympathetic ganglionic cells in the bowel –> may result in needing bowel resection
Hirschsprungs
Risk factors for the development of persistent pulmonary htn of the newborn
- birth asphyxia (most common) 2. maternal use of prostaglandin inhibitors near term (NSAID, ASA) 3. Diaphragmatic hernia 4. microthrombus
_________________ is associated with increased muscularization of pulmonary arterial vessels, sepsis, and aspiration syndromes
persistent pulmonary htn of the newborn
diagnosing persistent pulmonary htn of the newborn
- echo = shunting across PDA; tricuspid regurg 2. holosystolic murmur 3. hx by interview that indicates: meconium aspiration, abnormal FHR monitor 4. sx: cyanosis, respiratory distress with tachypnea but minimal retractions 5. lg shunt: PAO2 gradient > 20 mmHg
goals in treating persistent pulmonary htn of the newborn
- decrease PVR 2. improve oxygenation 3. correct acidosis 4. correct myocardial dysfunction
tx for persistent pulmonary htn of the newborn
- tx underlying cause 2. high frequency jet ventilation (HFJV) 3. Nitric Oxide (mainstay of therapy) 4. sildenafil (pulmonary VD) 5. inotropes 6. if HFJV & NO fail = ECMO
what is the only therapy/tx for severe combined immunodeficieny d/o (SCID)
stem cell transplant
__________________ is where both T cell and B cells are very low or absent causing infants to have recurrent and severe infections
severe combined immunodeficiency (SCID)
which pediatric d/o are autosomal recessive
- Hurlers 2. Cystic Fibrosis 3. Spinal muscular atrophy