Peds 3

Question 1

Classic finding in hypertrophic pyloric stenosis

Answer 1

Palpable olive-shpaed mass in abdomen
Low chloride levels
Metabolic alkalosis

Question 2

Diagnostic test in a stable patient suspected of pyloric stenosis

Answer 2

Abdominal sonogram

Question 3

First step after delivery or after stimulation on the radiant warmer

Answer 3

Dry the baby on mother’s chest

Question 4

Course of action when infant does not improve on radiant warmer, has irregular or no respirations, & HR < 100

Answer 4

Open the airway and provide positive-pressure ventilation w. oxygen

Question 5

Immediate intubation & suctioning of the trachea is warranted when the infant is depressed

Answer 5

W. thick, meconium stained amnniotic fluid

Unless the baby is crying which means the infants is unlikely to have severe meconium aspiration

Question 6

During neonatal evaluation, the HR is checked at what location.

Answer 6

Base of umbilical cord

Question 7

If HR < 100

If HR < 60

Answer 7

Bag & mask ventilation

Chest compression

Question 8

Course of action when the infant is active w. adequate respirations and HR during the ventilation but STAYS blue

Answer 8

Blow-by oxygen until the color improves

Question 9

Typical presenation of congenital hypothyroidism seen b/w 3-6 mon.

Answer 9

Most commonly due to thyroid dsygenesis 
Weak cough & prolonged jaundice are early signs 
Generalized hypotonia 
Slow respiratory effort 
Coarse facial features 
Enlarged fontanelles 
Poor feeding 
Somnolence 
Large tongue 
Constipation 
Umbilical hernia 
Dry, mottled skin

Question 10

Most common cause of congenital hypothyroidism

Answer 10

Thyroid dysgenesis

Question 11

Elevated serum tyrosine is seen in Type I tyrosinemia (AR) due to deficiency of hepatic fumarylacetoacetate hydroxylase

Answer 11

Present at 2-6 mon. w. acute hepatic crisis (fever, vomiting, hypoglycemia, hepatomegaly, hemorrhage, & jaundice) & cabbage-like odor dysp
Risk of HCC & cirrhosis w. age
Can lead to peripheral neuropahty & Fanconi syndrome

Question 12

Condition commonly occurs in children < 5yrs. & is characterized by diffuse scarlatiniform erythema, sterile flaccid blisters, positive Nikolsky sign, areas of desquamation (2-5 days after rash appears) that can increase risk of secondary infections & significant fluid and electrolyte losses but resolves in 2 wks. w/o scarring

Answer 12

Staphylococcal scalded skin syndrome

Treated w. penicillinase resistant nafcillin or oxacillin

Question 13

WAGR associations due to deletion of chromosome 11 w. peak incidence at 2-5 yrs.

Answer 13

Wilms tumor
Aniridia
Genitourinary abnormalities
Growth/developmental retardation