Peds Flashcards
0
Q
What are racoon eyes a sign of?
A
Neuroblastoma
1
Q
What cells is neuroblastoma derived from?
A
Precursor cells for the sympathetic pathway. Therefore it excretes catacholamines
2
Q
Congenital horners should raise suspicion for
A
Neuroblastoma bc it messes w the sympathetic pathway
Check urine catacholamines
Symp dilates
Therefore miosis
3
Q
What do eyes look like in primary position in browns syndrome?
A
hypotropia of effected eye
4
Q
Stumped
A
Sclerocornea Trauma (foreceps) Ulcer Mucopoly Peters Endothel dystrophy (ched 2 AR cloudy from birth) Dermoid
5
Q
on eom in browns what do you see
A
unable to elevate when adducted improves upon abduction
6
Q
how do you treat duanes surgically?
A
recess the (tight) medial rectus of effected eye
7
Q
how do you surgicaly treat upshoots and downshoots in duanes?
A
Y split of lateral rectus of effected muscle
8
Q
objects that fall on the horopter stimulate what?
A
corresponding retinal points
9
Q
whats kassebach-merrit syndrome
A
in capillary hemangioma there may be plt sequestration causing thrombocytopenia. so check cbc in kid w cap hemangioma
10
Q
diplopia in XT is crossed or uncrossed?
A
crossed (stimulates temporal retinas)
11
Q
diplopia in ET is crossed or uncrossed?
A
uncrossed (stimulates nasal retinas)
12
Q
is w4d more dissociating w lights on or off?
A
off
13
Q
if the eye is turned in, on what part of the retina does the image fall?
A
nasal
14
Q
pts w monofixation will fuse w4d at near or distance?
A
4 lights at near, 2 lights at distance
15
Q
who gets monofixation syndrome?
A
post-op congenital ET who has small residual ET
16
Q
whats the most “dissociating test” that you can use to test for arc? (most dissociative means least like an everyday binocular use of eyes
A
afterimage test (tests each eye individually and tags the fovea w vertical line in one eye and horizontal line in the other)
17
Q
if you give an after image test and you see an X what does that mean
A
you have NRC
18
Q
order these tests from most dissociative to least
red glass, bagolini, after image, amblyoscope, w4d
A
afterimage- most w4d red glass amblyoscope bagolini- least
19
Q
How many layers are there in the LGN?
A
6
20
Q
if pt has a strong fixation preference and cannot hold fixation with one of their eyes what does it mean about that eye?
A
it is amblyopic
21
Q
whats the type of ambly with congenital ptosis?
A
aniso ambly 2/2 astigmatism
22
Q
how many seconds of stereo is perfect stereo?
A
40 sec
23
Q
how do you deternine when to operate on someone with X(T)? based on pd?
A
no, its all based on whether they can control the X(T) or not. Not how big it is
24
why would you give a kid over-minus glasses?
if they are XT it will cause them to accommodate more and converge more
25
whats the normal value of AC:A ratio?
5
26
what surgery do you for X(T)
LR recession OU
27
Whats the surgery for sensory XT?
R&R on amblyopic eye
28
when do you get A and V patterns?
in et or xt
29
what surgery would you do for XT w big V- IO overaction?
LR recession OU with IO weakening OR you could move the medials to the apex of the V and laterals the opposite way (MALE)
30
What chin position would a kid do if they had an A pattern?
chin down
31
how do you treat an XT with mild A pattern (ie SO overaction)
SO surgery is fraught with problems.So don't tough them, instead do MALE surgery
32
whats the formula to calculate AC:A ratio?
```
IPD(cm) + N-D/Diopters of accommodation
IPD= interpupillary distance
N= ET in PD at near
D= ET in PD at dist
Diopters = 3
remember to convert IPD from mm to cm
```
33
whats the Parks rule for determining if there is high AC:A ratio?
if their ET at near is 10PD greater than their ET at distance its accommodative eso
34
whats the treatment for acomodative eso?
glasses! give full plus
35
when do you give bifocals?
straight eyes in distance and big ET at near. So at distance they look thru plano and at near they get plus so it relaxes accomodation
36
how does plus glasses relax accommodation?
it gives you + power, so you don't have to accommodate to make your own + power
37
when do you operate on an ET and do you operate for the PD cc or sc?
operate for the deviation with glasses on. Only operate if they still have ET even with full spectacle . tell them they will need glasses even after surgery
38
whats cyclic esotropia and how do you treat?
kid who is ET one day and straight the next. Generally has a 24 cycle. Operate for the full ET, do not patch! Will cause the ET to become constant
39
whats hypermetropia?
synonym with hyperopia
40
how do you treat infantile ET?
try full + glasses first
41
what are the 3 bad complications after treatment of congenital et?
1) DVD
2) latent nystagmus
3) IO overaction
42
what rule does DVD violate?
herrings law. its like you take a saw and divide your head. The eyes don't coordinate
43
what direction is latent nystagmus?
fast phase toward the fixing eye
44
do kids with congenital ET have any chance for high grade stereopsis?
not a chance. At best they can become monofixators (small central suppression/scotoma)
45
whats smooth pursuit asymmetry?
normal kids develop smooth pusuit from temporal to nasal direction first. once they get older they can follow nasal to temporal. Kids with ambly never develop good nasal to temporal pursuit
46
how often can infantile ET resolve
almost never. only 4%
47
whats the forced generation test?
put in proparacaine, grob eye w .12 and tell them to look in each direction and feel if the eye is generating force
48
how do you treat a vascular or traumatic cn6 palsy?
observe 6 months
49
what surgery can you do for cn6 palsy?
1) hummelsheim procedure. split both the SR and IR and transpose part of it to the insertion of the LR
2) Jensen- split the LR and sew the muscle itself to the SR and IR
51
Whats double elevator palsy?
actually a monocular elevation problem
Tight IR (restrictive) vs. paralysis
Causes unable to look up in adduction and abduction (unlike browns has prob w elevation in adduction only)
51
Whats the main cause of acquired browns sx?
Sinusitis
52
How do you treat double elevator palsy?
if restrictive- recess IR
| If paralytic- do Knapp procedure. Bring the MR and LR up next to the SR
53
How do you work up acquired browns?
Image the orbit
54
What does it mean if you have a hyper and the hyper is worse on tilt toward that side?
It must be an oblique problem!!!!
55
If a kid has a left hyper worse on left head tilt, what are the 2 options of which muscle is bad?
Left SO
| Right IO
56
What will someone w congenital so palsy look like?
Will have head tilt and facial asymmetry able to fuse hyper
57
How do you treat congenital so palsy?
Weaken ipsilater io
58
Whats a bad complication of anyeriorizing the io to much?
Anti elevation syndrome
| Bc the io elevates if you weaken too much you fuck it up
59
Why do you do a harada ito procedure?
Produces intorsion
60
whats a typical stereoacuity in monofixation syndrome?
2000 sec of arc (not good)
61
when would you operate on 1 muscle vs 2 muscles?
if the deviation is > 25PD you have to operate in 2 muscles
62
what do you do if a baby doesn't FF at 5 mo?
observe. if still not FF at 1 yr do VEP
63
whats the definition of ophthalmia neonatorum?
conjunctivitis in 1st month of life
64
oil droplet cataract associated w?
galactosemia
65
what type of cataract in alports syndrome?
ant lenticonus
66
what type of cataract in downs?
cerulean "blue dot" cataract
67
discaform cataract associated with?
lowes syndrome (x-linked recessive, MR, glaucoma)
68
how is lowe's inherited, whats the synonym, and what type of cataract
x-linked
oculocerebrorenal syndrome
discaform (50% will have cat and glaucoma)
69
for any et or xt of 15PD, how far back should your R&R be on the LR AND MR?
MR 3mm
| LR 4mm
70
you do a goniotomy for a kid- it doesn't work. Whats the next step?
another goniotomy!
71
in what order do these causes of ophthalmia neonatorum present themselves? chlamydia, chemical, gonnorhea, hsv
chemical- first 24 hrs
gonorrhea- 2-3 days
chlamydia- 5-7 days
hsv- 2 weeks
72
what's megalocornea? (besides glaucoma)
x-linked condition in boys. random. moms can have enlarged K nerves
73
which antiemetic is totally contraindicated in kids <2
promethazine (resp depression- its like meth for kids)
74
which babies get screened for rop?
<1500 grams (3.3 lbs)
75
kids with myelinated rnfl are at risk for what type of amblyopia
refractive
76
Mass superior to medial canthus worry abt
Meningocele!!!!
| Superior= coming from brain
77
homocystinurea- inher pattern, how do the kids look, which way does lens dislocate, complication of surgery
AR
Tall blonde with MR
inf-nasal dislocation
hypercoaguability
78
upper eyelid coloboma is associated with what syndrome?
goldenhaar
79
upper eyelid coloboma is associated with what syndrome?
goldenhaar
80
whats another name for posterior lenticonus and is it uni or bilateral?
oil droplet cataract
| unilateral
81
whats a test beside an MRI that you can use to check for neuroblastoma?
urinary catecholamines
82
when do you take out
1) unilateral congenital cat
2) bilateral congenital cats
1) before 6 weeks old
| 2) before 10 weeks old
83
whats the primary, secondary and tertiary fxn of the SR?
1) elevation
2) intorstion
3) adduction
84
whats the inher of oculocutaneous albinism?
AR
85
Whats the difference between tyrosinase-pos and tyrosinase-neg?
tyrosinase negative has worse prognosis bc complete lack of pigment
86
whats the difference between oculocutaneous albinism and ocular albinism
ocular albinism occursonly in boys bc its X-linked recessive
87
what chromosome is associated with RB?
13
88
What chromosome is associated with alveolar rhabdo
cross between chrom 1 and 13 (13 is the rb chrom)
89
what tumor has antoni A and B cells?
Schwannoma
90
FGFR gene associated with what syndrome?
crouzons
91
how does patau syndrome (trisomy 13) present?
Microphthalmos
MR
Polydactyly
dwarfism
92
how are the Y sutures oriented in the lens?
upright Y anteriorly
| inverted Y posteriorly ((posterior for peace")
93
what do you have to worry about when you put a pt w weill-marchesani under general anesthesia?
thromboembolic events
94
Most common indication for PK in kids?
peters
95
what diameter of K should make you suspicious for congenital glaucoma?
>12
96
describe the kestenbaum procedure
try to align eyes TOWARD the head turn, so if kid has left head turn, would resess LLR, RMR etc.
97
which has the worst gram + coverage?
ceftaz
98
whats the inheritance of ectopia lentis et pupillae?
AR (a closed pupil recesses you ability to see)
99
what molecule is defective in marfans?
fibrillin
100
in what dz do you give low methionine and high cysteine?
homocystinuria (AR, with MR, tall, seizures)
101
inheritance of fabrys
x-linked recessive (Fabulous HUNTER- x links the spot)
102
when do you screen rop kids?
4-6 weeks post-natal OR
| 31-32 wks GA
103
if you have a kid straight in dist but has accom ET- how do you treat?
give bifocal glasses
| no surgery if they are straight in the distance
104
how do you treat infantile ET?
Give full +
| if still have ET even with glasses then surgery
105
how much ET do you operate for in accommodative ET?
Operate on the Dist cc (The augmented way is to operate on the avg value bet the Nsc and Ncc)
106
how do you treat cyclic esotropia?
operate on the full deviation on the bad day
107
right hyper, what are the 4 possible effected muscles?
RSO
LIO
RIR
LSR
108
what does the harada ito procedure do?
strengthens fibers causing intorsion
109
Right hyper WORSE ON LEFT HEAD TILT what are the 2 possibilities?
RIR- hyper will be worse with right gaze
| LSR- hyper will be worse with left gaze
110
right SO palsy what are parks 3 steps
Right hyper
Left gaze worse
Right head tilt worse
111
how does x-linked dominant work?
need only 1 X to get the dz so both boys and girls can get it
112
how does x-linked recessive work?
mom is the carrier of 1 bad X
boys get the bad X from mom and get dz
girls end up being carriers
113
what are the primary, secondary and tertiary fxns of the SO? (SO-LID)
1) intortion
2) depression
3) lateral movement of the eye
114
weill marchesani- inher and cataract type
AR
microspherophakia
short
flat head
115
galactosemia- inher, type of cataract
AR
| oil-droplet (aka post lenticonus)
116
most common manifestation of fabrys in the eye
K verticilata (x linked)
117
myelinated rnfl ass with what syndrome
basal cell nevus syndrome (they dev bccs)
| or ipilateral high myopia
118
how can you differentiate browns from IR restriction
there will be restriction with retropulsion in browns
119
CHED1 vs CHED 2- inheritance, how does it present?
ched 1- AD presents at 1-2 yo, progresses slowly
| ched 2- AR cloudy from birth
120
congenital stroma corneal dystrophy- inher and how does it present?
AD
| flaky things in stroma, doesn't get worse
121
what did the beat ROP study show?
that IVA was better than laser for stage 3 zone 1 rop
122
what chediak higashi syndrome
recurrent pyogenic infections ass with albinism
123
whats hermansky pudalk
platlet pooling problem leading to bleeding in Puerto Ricans w albinsim
124
Whats waardenberg sx?
Neural crest dz
Iris heterochromia (brilliant blue eye)
White forelock
Deafness
125
What dz ass w pax 6?
Peters
Aniridia
Coloboma
Microphthalmia
126
Skew deviation (2/2 bad vestibular input) looks like CN4 palsy in every way except
the effected eye will be INCYCLOTORTED! that is not c/w cn4 palsy
127
besides the 3 step test for cn4 palsy, what other deviation can you find w 4th?
v pattern eso (worse in downgaze!)
128
can peters be associated with glaucoma?
yes!
129
whats peters plus?
peters w systemic anomalies- facial cardiac, polydactyly
130
posterior lenticonus present at birth?
no
they are unilateral and acquired
ass w galactosemia
131
alports- inheritance, signs and retina finding
x-linked dominant
glomerulonephritis
high-tone deafness
"dot and fleck" retinopathy
132
in latent nystagmus when you occlude one eye what happens to the velocity of the nystagmus
DECREASE in slow phase velocity
133
in congenital nystagmus what happens to the velocities over time?
INCREASE in the slow phase velocity
134
whats the definition of megalocornea?
>13mm in diameter
135
what dz can be associated with megalocornea?
marfans
136
kids w forecep injury lose vision from what
astigmatic amblyopia (the k edema from the forceps resolves quickly so its not the cause of the ambly)
137
whats the general surgical approach to duanes?
RECESS the muscle that's actually working in the effected eye.
138
2 diseases associated w Christmas tree cataract
myotonic dystrophy
| hypoparathyroidism (low ca levels)
