Pediatrics

Question 1

What’s the second most common cause of stridor in neonates?

Answer 1

Vocal cord paralysis

Question 2

Which IGg deficiency associated with susceptibility to encapsulated bacteria

Answer 2

IGG2

Question 3

In adults what is the most common IGg deficiency

Answer 3

Igg3 susceptibility to uri, AR and asthma

Question 4

What are the centor criteria for GABHS in children

Answer 4

Fever, tender neck adenopathy, exudative tonsillitis, and absence of cough

Question 5

What is Melnick Fraser syndrome

Answer 5

Branchial-oto-renal

Question 6

What is the treatment for Kawasaki disease?

Answer 6

Ivig and aspirin

Question 7

Symptoms of Usher Type 1

Answer 7

retinitis pigmentosa, profound SNHL from birth, vestibular dysfunction

Question 8

Symptoms of Usher type 2

Answer 8

SNHL in adolescence, NO vestibular dysfunction, no retinitis pigmentosa, most common syndromic form of hearing loss

Question 9

Usher type 3

Answer 9

Similar to 1 but milder symptoms, progressive hearing loss, visual loss at puberty

Question 10

What is the most common IgG class deficiency in children?

Answer 10

IgG2, predisposes to recurrent infections to polysaccharide encapsulated bacteria such as H Flu, strep pneumo, and klebsiella

Question 11

What is the most common IgG deficiency in adults?

Answer 11

IgG3

Question 12

Branchial groove/cleft corresponds to which embryonic cell derivative?

Answer 12

Ectoderm

Question 13

Branchial arch is what embryonic cell derivative?

Answer 13

Mesoderm

Question 14

Branchial pouch corresponds to which embryonic cell derivative?

Answer 14

Endoderm

Question 15

What are the four types of VPI closure?

Answer 15

° Coronal (55 %, most common) ° Sagittal (10–15 %, least common) ° Circular (10–20 %) ° Circular with Passavant’s ridge (15–20 %)

Question 16

What is prominauris

Answer 16

absent antihelical fold, abnormally distal insertion of antitragus muscle, excess conchal bowl

Question 17

What does CATCH-22 stand for in DiGeorge Syndrome?

Answer 17

Cardiac defects, Abnormal facies, Thymic hypoplasia, Cleft palate, and Hypocalcaemia resulting from 22q11 deletions.

Question 18

What percentage of parotid neoplasms in children are malignant?

Answer 18

50%

Question 19

What are the most common locations of rhabdomyosarcoma in descending order

Answer 19

Orbit Nasopharynx Middle ear/mastoid Sinonasal cavity

Question 20

What syndrome is PAX3 gene mutation associated with?

Answer 20

Waardenburg

Question 21

Mnemonic for autosomal dominant syndromes

Answer 21

WANTBCS

Question 22

normal anatomy of the ear in pediatrics

Answer 22

Normal anatomy: 15- to 30-degree posterior angulation, auriculocephalic angle of 20 to 35 degrees; normal pinna position is 15 to 20 mm from the helical rim to the scalp

Question 23

When are lymphatic malformations diagnosed

Answer 23

40% in neonatal period, 60% by age 1, 90% by age 3

Question 24

stain for bartonella?

Answer 24

Warthin starry silver stain

Question 25

What is a pilomatrixoma?

Answer 25

Calcifying epitheolioma of malherbe Arises from the outer root sheath sell of hair follicle

Question 26

What is the most common malignancy in infants less than 1 year of age?

Answer 26

Neuroblastoma

Question 27

Is coronary artery aneurysm an early or late symptom of kawasaki disease?

Answer 27

Late

Question 28

During which week of development does the EAC recanalize?

Answer 28

28th week

Question 29

During which week of development do the hillocks of his develop, and then by which week do they fuse to form the auricle?

Answer 29

6th week, 12th week

Question 31

What is the likelihood of a negative bronch in the setting of unwitnessed choking episode?

Answer 31

60%

Question 32

What is the blood supply to the adenoid

Answer 32

Pharyngeal branch of the internal maxillary (major supply) Ascending palatine branch of the facial artery Ascending cervical branch of thyrocervical trunk Ascending pharyngeal artery

Question 33

What are the most common sites of rhabdo in descending order

Answer 33

Orbit Nasopharynx Middle ear/mastoid Sinonasal cavity

Question 34

which type of rhabdo has better prognosis: embryonal or alveolar?

Answer 34

embryonal (75% of them)

Question 35

what is Von-Hippel-Lindau

Answer 35

° Autosomal dominant ° Hemangioblastomas of CNS and retinas, renal cysts/carcinoma, pheochromocytoma, pancreatic cysts, papillary cystadenomas of epididymis ° Associated with endolymphatic sac tumors

Question 36

What is maffucci syndrome?

Answer 36

benign cartilagenous overgrowths

Question 37

What are the two most common syndromes associated with PRS?

Answer 37

Stickler, velocardiofacial syndromes