Pediatrics Flashcards
Types of congenital heart disorders
CYANOTIC (5T's + others) Truncus arteriosus Transposition of Great Vessels Tricuspid valve abnormalities Tetralogy of Fallot Others: Pulmonary atresia Hypoplastic Left Heart Syndrome
NON-CYANOTIC VSD PDA ASD Coarctation of aorta
4 features of Tetralogy of Fallot
- Ventricular septal defect
- Right ventricular hypertrophy
- Pulmonary stenosis
- Overriding aorta
Classic CXR of Tetralogy of Fallot
boot shaped heart due to RVH
What is pulmonary atresia?
congenital pulmonary valve closure
Cyanotic vs non-cyanotic congenital heart disorders
cyanotic: R to L shunting; deoxygenated blood returns from body and bypasses lungs and is recirculated
non-cyanotic: L to R shunting; blood skips the body
Pathophysiology of Hypoplastic Left Heart Syndrome
small undeveloped left ventricle and aorta
right side of heart pumps blood to the body through a patent ductus arteriosus
Congenital heart defect with crescendo-decrescendo holosystolic murmur along the left sternal border and radiating to back?
pulmonary stenosis of Tetrology of Fallot
Pathophysiology of Transposition of Great Vessels
complete transposition of pulmonary artery and aorta
What is an overriding aorta?
aorta attaches to both right and left ventricle
How are all cyanotic congenital defects treated?
surgery
Common cause of atrial septal defect?
foramen ovale doesn’t close or is too large
ECG findings of atrial septal defect
RVH, R bundle branch block
How to definitively diagnose congenital heart defects?
ECHO
What does the ductus arteriosus connect? Function?
pulmonary artery to aorta
allows for most blood to bypass lungs in utero
Pathophysiology of PDA
ductus arteriosus should close at birth, but in PDA it is patent/open
Treatment of PDA in neonate and after birth
neonate - NSAIDs
first 10-14 days of life - IV indomethacin
Congenital defect of aorta narrowing
coarctation of aorta
Congenital heart defect with machine-like murmur
PDA
What keeps ductus arteriosus open in PDA?
prostaglandins
PE findings coarctation of aorta
failure to thrive
delayed or weak femoral pulse
harsh systolic murmur
HTN in upper extremities and hypotension in lower
Treatment of ASD
small shunt may require no treatment
larger defect may need surgical closure
You are working in the free pediatric clinic. A one week old infant is brought it to see you. Upon listening to his chest you notice a systolic ejection murmur in the 2nd and 3rd intercostal spaces. There also seems to be an early to mid systolic rumble. What is your diagnosis?
Atrial septal defect
Ballard score
newborn assessment of activity, position, and tone to evaluate neuromuscular and physical maturity
rubric estimates gestational age
Causes of infant’s being small for gestational age
maternal drug use, chromosomal abnormality, viral infection, multiple birth, advanced maternal age, placental insufficiency, or lack of maternal weight gain
What is advanced maternal age?
> 35 yo
Most common cause of being large for gestational age
maternal diabetes
When should complete newborn exam be done?
within 24 hrs of birth
erythema toxicum
common rash in newborns 3-5 days old
small pustules with erythematous bases
spontaneous resolution in 1-2 wks
milia
common newborn rash
very small, white papules mostly on face
resolves w/o treatment in 1-2 months