Pediatrics 2 Flashcards
What will be formed by failure of obliteration of 2nd brancheal cleft?
BRANCHIAL CYST
- cystic mass in lateral aspect of neck
- may open with fistula
- remove by surgical excision
cystic mass at line of fusion is called?
SEQUESTRATION DERMOID CYST
- usually occurs in external angular in face
- if in neck -> median
- treated -> simple excision of cyst
unilateral sternomastoid mass after birth trauma?
congenital torticollis
- diagnosed by neck US
- head tilt to same side
coarse lymphangioma presenting with large, translucent cystic mass at the side of the neck is called?
CYSTIC HYGROMA
- inject sclerosing agent
What are the types of congenital diaphragmatic hernias?
POSTERIOR HERNIA -> foramen of Bockdalek (commonest type)
ANTERIOR HERNIA -> Foramen of Morgagni (opening of IMA)
DIAPHRAGMATIC EVENTRATION -> weakness
CONGENITAL HIATUS HERNIA
What is the clinical presentation of a congenital diaphragmatic hernia?
ANTENATAL -> maternal polyhydraminos
AT BIRTH -> neonatal cyanosis & respiratory distress
- scaphoid abdomen
- diminished air entry with audible intestinal sounds on chest
- heart sounds heard better on right side
What are the complications of a congenital diaphragmatic hernia?
- ipsilateral pulmonary hypoplasia
- contralateral lung compression
- strangulation
What investigations should be done in order to diagnose a diaphragmatic hernia?
CHEST X-RAY
- bowel in chest
- shift of mediastinum to contralateral side
- dextrocardia
GASTROGRAFIN MEAL
ANTENATAL US
- polyhydramanos
BLOOD GASES
- hypoxia
- hypercapnia
- acidosis
What is the most important step in treatment of congenital diaphragmatic hernia?
PRE-OP PROPER PREPARATION
- NPO
- NGT & IV FLUIDS -> deflate stomach -> decrease lung compression & mediastinal shift
- endotracheal intubation -> if failed -> ECMO
- pulmonary vasodilators
What is the definitive treatment of a congenital diaphragmatic hernia?
OPERATIVE REPAIR AFTER PRE-OP PREP
- open -> subcostal incision OR thoracoscopic -> reduce abdominal contents & fix diaphragmatic defect
What is the cause of esophageal atresia?
failure of recanalization of the foregut
What are the types of esophageal atresia?
- blind upper pouch & fistula of lower pouch -> most common
- upper fistula & lower atresia
- atresia without fistula
- fistula without atresia
- atresia with upper & lower fistula
What are the complications of fistulas?
- lower fistula -> fatal acid pneumonia
- upper fistula -> aspiration of milk & saliva
cause of death -> pneumonia or VACTREL
What is the clinical picture of esophageal atresia?
antenatal -> maternal polyhydraminos
at birth -> CONTINUOUS POURING OF FROTHY SALIVA SINCE BIRTH
-> regurgitation, chocking, cyanosis & cough
- CATHETER TEST -> stops at 10cm from nostrils
- abdominal distention -> due to air entry
- dehydration
- pneumonia
What investigations should be preformed to diagnose esophageal atresia?
X-RAY -> fundic air bubbles increase
GASTROGRAFIN -> shows atresia