Pediatric ENT Flashcards
1st branchial arch nerve + derivatives
CN V
Mandible, Meckel’s cartilage –> malleus (except manubrium), body + short process incus, tensor tympani, mastication muscles, mylohyoid, anterior belly digastric, tensor palati muscle
2nd branchial arch nerve + derivatives
CN VII
Reichart’s cartilage –> Manubrium malleus, long process incus, all of stapes except footplate (all stapedial artery, styloid process, lesser cornu of hyoid, stapedius muscle, facial muscles, posterior belly of digastric
3rd branchial arch nerve + derivatives
CN IX
Greater cornu of hyoid, stylopharyngeus muscle, sensory to posterior 1/3 of tongue, superior + middle constrictors, CC a., ICA
Pouch: Inferior parathyroids, thymus
4th branchial arch nerve + derivatives
Superior laryngeal nerve
Thyroid cartilage, inferior pharyngeal constrictor, cricopharyngeus, cricothyroid muscles, left aorta, subclavian on right
Pouch: Superior parathyroids, ultimobranchial body (C cells)
6th branchial arch nerve + derivatives
Recurrent laryngeal nerve
Cricoid, arytenoids, corniculate, trachea, intrinsic laryngeal muscles, ductus arteriosis
6 Hillocks of His
1st Arch
1 - Tragus
2 - Helical root/crus
3 - Helix (rim)
2nd Arch
4 + 5 - Antihelix
6 - Antitragus
*Preauricular cyst arises from partial failure of involution of epithelium between 1st and 2nd hillocks
Chandler classification (1-5)
- Preseptal involvement (EOMI, no visual changes)
- Orbital Cellulitis (NO abscess)
- Subperiostial abscess (between orbital periostium and bony orbital wall). Displaces orbit down and lateral (proptotic). Associated with limited EOM and vision changes
- Orbital abscess
- Cavernous Sinus Thrombosis - BILATERAL SX
Complications of persistent sinus disease
-Orbital (chandler classification)
-Intracranial (meningitis, epidural abscess, subdural abscess, acute and chronic brain abscess) –> meningitis is the most common!
What is Cidofovir and what is it used for?
DNA polymerase inhibitor, used off label for respiratory papillomatosis
What is Bevacizumab and what is it used for?
VEGF inhibitor, used off label for respiratory papillomatosis
What HPV subtypes cause respiratory papillomatosis?
HPV 6 and 11
Most common cause of pediatric otitis media (bugs)
Strep pneumo, H inluenza, Moraxella, Group A Strep
Indications for T tube placement
-Chronic OME > 3 months bilaterally or >6 months unilaterally
-Earlier if severe, significant HL, speech delay, severe retraction, vestibular SX, has complications from OM
Top 4 bugs for acute mastoiditis
S. pneumo, H influenza, Strep pyogenes, S. Aureus
Indications for bone conducting hearing aids
Atresia or microtia (can’t use traditional), CHL with AB gap > 30 dB, Mixed HL (BAHA can compensate for up to 65 dB HL), SS deafness, inability to fit traditional hearing aid because of skin allergy or chronic draining ears
Features of nose in cleft lip
-Posterior septum deviated TOWARD the cleft
-Nasal tip, anterior septum and base of columella deviate AWAY from the cleft
-Nostril on the cleft side is flattened and stretched inferiorly
and laterally (nostril is horizontal)
-Cleft side has SHORTER medial crus + LONGER lateral crus (lateral steal phenomenom)
-Cleft side lower lat cartilage is displaced inferolaterally + posteriorly
-Incomplete orbicularis oris sphincter
Timeline for infantile hemangiomas
Appear in first few weeks of life –> grow rapidly over a few weeks –> continue to grow over 6-9 months –> then involute over the next few years.
What factors are present during proliferation of infantile hemangiomas?
-Always GLUT-1 positive
-VEGF, type IV collegenase, insulin like GF, fibroblast GF all increase during proliferation. Everything but fibroblast gf decrease during involution.
Two type of congenital hemangiomas?
- Rapidly involuting (RICH)
- Noninvoluting (NICH)
What is PHACES?
Posterio fossa abnormalities (Dandy-walker), hemangioma (congenital, segmental), arterial abnormalities, cardiac and aortic abnormalities, eye abnormalities (cataract), sternal clefts.
What percent of beard distribution hemangioma are associated with airway involvement?
65%
Treatment for hemangiomas
Propanolol - 1st line
-Steroid - only if fail propanolol or for local injection
-Surgical excision (if non involuting, ulcerating, pedunculated so unlikely to involute, or disfiguring/causing distress)
-CO2 vs Yag laser (though overuse can cause subgottic stenosis)
What is Kasabach-Merrit Syndrome?
-Associated with vascular hemangiomas (kaposiform or tufted hemangioma).
-Rare, tumor traps and destroys platelets + other coagulopathies.
-TX - Chemotherapy (vincrystine)
Timeline of vascular malformations
Present at birth and grow with age of child (so not rapid).
Features of Sturge Weber syndrome?
-Vascular malformation
-Facial port wine stain in trigeminal nerve distribution, glaucoma/eye abnormalities, ipsilatral intracranial malformation.
-Children often develop seizures, migraines, stroke, hemiparesis, vision issues, etc.
-TX: PDL to help with port wine stain, Yag laser if deeper, surgical debulking also an option + medical management for the health issues.
What is PFAPA + treatment?
Periodic fever, apthous stomatitis, pharyngitis, adenitis.
Adenoidectomy is highly effective at resolving this condition. Otherwise NSAIDS, consider steroids.
Criteria for abnormal sleep study for pediatric patients?
AHI 1-5: Mild
AHI 6-10: Moderate
AHI > 10: Severe
O2 desat to below 92%
Peak end tidal CO2 > 53 mmHg
Elevated end tidal CO2 > 50 mmHg > 25% of total sleep time.
Indications for tonsillectomy?
Recurrent infections (7 in 1 year, 5 per year for 2 years, 3 per year for 3 years), PTA, chronic tonsillitis, obstruction, sleep disordered breathing, OSA, PFAPA, craniofacial growth abnormalities, dysphagia, Cor Pulmonale
Indications for post op sleep study?
Persistent symptoms, AHI > 20, pre op complication of OSA (pulm HTN), Age < 1 year
Max dosage for lidocaine (without epi) in kids?
3-5 mg/kg
Treatment for prominauris?
-Mustart technique to recreate antihelical fold (three horizontal mattress sutures to secure auricular cartilage to itself, no incisions). Each horizontal mattress suture is placed 2 mm apart and involved 16 mm distance across antihelical fold with 1 cm bite width.
-Furnas technique to reduce conchomastoid angle (secure conchal cartilage to mastoid periosteum)
Issue = large auricocephalic angle (ear sticks out more than 25-35 degrees), abnormal distal insertion of anti tragus muscle.
SX, TX and mortality rate for untreated Kawasaki?
SX - strawberry tongue, conjunctivitis, coronary artery aneurysms, cervical lymphadenopathy, fever.
TX - IVIG + Aspirin
Mortality untreated - 1%
What is mobius syndrome? What is a potential surgical treatment?
-Incomplete development of FN 6 and 7 (and absence of FN 7 in the IAC).
-Bilateral facial nerve paralysis
-TX - Temporalis muscle sling (can’t do any nerve grafts)
Crouzon
-AD, FGFR mutation
-Craniosynostosis
-Midface hypoplasia
-Ocular proptosis, parrot beak nose
-CHL (due to stenosis and stapes fixation
Apert Syndrome
Apert: AD, FGFR mutation, all of Crouzon PE + limb syndactyly.
Pfeifer: All of Crouzon PE + broad thumb + toes.
Stains for rhabdomyosarcoma?
Z bands
Stains positive for vimenting, myoglobin, desmin
Microcystic vs macrocystic lymphatic malformations (location, characteristics).
Microcystic - usually suprahyoid. More difficult to treat (more extensive infiltration of surrounding soft tissues). More likely to recur. TX - excision or sclerotherapy
Macrocystic - thick walled cysts, less infiltrative. Easier to excise. Less likely to recur. Infrahyoid.
Features of choanal atresia
F>M
Unilateral > Bilateral
Usually BONY defect (90%)
Associated with CHARGE, Apert, Treacher Collins, Trisomy
First Branchial Cleft Cyst
Three types?
When to get hearing test?
Excision steps?
I - Inferoposteromedial to pinna (ectoderm only)
II - Between angle of mandible and EAC (ectoderm and mesoderm)
III - Periparotid
Tract runs in close proximity to facial nerve (medial or lateral) –> would need FN dissection
*Don’t forget formal hearing test for bilateral or family history even if not planning for surgical excision.
Excision: Ellipse around the cyst, dissect down to helical root and INCLUDE perichondrium/cartilage to help reduce risk of recurrence.
2nd Branchial Cleft Cyst
What side is it most common on?
Course?
Most common (more common on RIGHT)
Anterior to SCM, BETWEEN ICA and ECA, deep to FN, superficial to CN 9 and 12, opens into tonsillar fossa
*Monitoring is appropriate if asymptomatic.
3rd Branchial Cleft Cyst
What side is it most common on?
Course?
External opening at lower anterior neck –> Passes posterior to ICA and ECA, superficial to CN X and common carotid artery, between CN IX (deep to it) and CN XII –> pierces thyrohyoid membrane staying above superior laryngeal nerve –> internal opening at APEX piriform sinus
*Fourth branchial cleft cyst is similar but STARTS as the BASE of the piriform sinus, ends @ anterior border of SCM. Very rare.
*Both are more common on the LEFT
Thymic cyst
Remnant of third pharyngeal pouch between angle of mandible and midline neck
SSx: unilateral (usually left) neck mass
Dx: biopsy, serum calcium (associated parathyroid disorders, DiGeorge syndrome/22q11), CT/MRI
Rx: excision