🚼 PEDIA PEARLS

Question 1

Bilateral Cafe-au-lait spots

Answer 1

Von Recklinghausen

Question 2

Coast of maine appearance

Answer 2

McCune Albright Syndrome

Question 3

Tx of McCune Albright Syndrome

Answer 3

Leuprolide acetate

Question 4

Manifested by polyuria (>5cc/k/hr) and polydypsia

Answer 4

Diabetes insipidus

Question 5

Vasopressin deficiency of DI

Answer 5

Central DI

Question 6

Vasopressin insensitive kidneys of DI

Answer 6

Nephrogenic DI

Question 7

Location of pituitary gland

Answer 7

Sella turcica

Question 8

2 lobes of pituitary

Answer 8

Anterior lobe (adenohypophysis)

Posterior lobe (neurohypophysis)

Question 9

The most common type of tumor in pituitary in children

Answer 9

Craniopharyngioma

Question 10

Most common type of tumor in pituitary in adults

Answer 10

Prolactinoma

Question 11

Anterior lobe hormones

Answer 11

ACTH

Growth hormone

Prolactin

TSH

LH

FSH

Question 12

Posterior lobe hormones

Answer 12

Vasopressin (antidiuretic hormone)

Oxytocin

Question 13

Underproduction of GH alone or in combination with other pituitary hormones

Answer 13

Hypopituitarism

Question 14

Absent or low levels of GH

Answer 14

Hypopituitarism

Question 15

Found in the nuclei of somatotropes, lactotropes and thyrotropes.

Answer 15

PROP1

Question 16

A nuclear protein that binds to the GH and prolactin promoters.

Answer 16

POU1F1 (formerly P1T1)

Question 17

Precocious puberty

Polyostotic fibrous dysplasia

Unilateral Cafe-au-lait spots

Answer 17

McCune Albright Syndrome