Peads surgery Flashcards
At what age would duodenal atresia present?
Few hours after birth
Association of duodenal Atresia
Trisomy 21 (30%) Cardiac/renal/other GI defects, Annular pancreas VACTERL
Presentation of duodenal Atresia antenatally?
Dilated stomach and first part of duodenum showing double bubble sign on USS
Presentation of duodenal atresia postnatally?
Early bilious vomiting in post-natal period (unless “pre-ampullary” atresia = non-bilious vomiting) Dilated stomach and first part of duodenum ‘Double-bubble sign’ on AXR
Management of Duodenal Atresia
NG tube
IV resusitation
Look for associated anomalies
Surgical duodeno-duodenostomy
What is this showing?
Double Bubble in Duodenal Atresia
Difference between presentation of malrotation vs malrotation with volvulus?
Malrotation - bilious vomiting, well baby (ladd’s bands obstruct duodenum)
Volvulus - bilious vomiting, unwell baby, peritonitis, metabolic acidosis *SURGICAL EMERGENCY*
At what age would malrotation with volulus present?
3-7 days after birth
Investigation of malrotation?
AXR can show paucity of distal gas; usually diagnosed by UGI contrast (if baby stable enough to perform)
Mnagement of malrotation?
Fluid resuscitation
Broad spectrum antibiotics
Immediate “Ladd’s procedure” – counter-clockwise detorsion of bowel and widening of mesentery
When would meconium ileus present and what does it mean?
- Meconium with abnormal mucous and enzyme content becomes solid and obstructs the gut antenally, presents in first few days of life
- Pathognomic of cystic fibrosis - represents more severe phenotype
Mnagement of meconium ileus?
Appropriate resuscitation
NG tube
Contrast enema may disimpact, as can N-acetylcysteine (PR and NG)
Laparotomy and evacuation of meconium may be required
what is the presentation of necrotising entoerocolitis?
Ischaemia and infection of the bowel in newborn. Leads to perforation, peritonitis, overwhelming sepsis
Predisposing factors: prematurity, formula feeds, respiratory distress syndrome, asphyxia, sepsis
Babies present with feed intolerance, bilious vomiting, abdominal wall discolouration, blood in stools, sepsis
What would an AXR show for necrotising entoerocolitis?
AXR shows pneumatosis intestinalis, portal venous gas, “fixed loop”, football sign (indicates perforation)
Management of enterocoliits?
Uncomplicated NEC: treat with antibiotics, gut rest, supportive care (7-10 days)
Surgical: can be difficult decision, perforation is absolute indication, mortality 25-40%