Pathoma congenitas Teratology, transpos, TA, tricuspid, coarct 12/04 Flashcards
4Fallot. Characterized by? 4.
- Stenosis of the right ventricular outflow tract.
- right ventricular hyperthrophy
- VSD
- aorta that overrides the VSD
4Fallot.
1…………..
2. right ventricular hyperthrophy
3. VSD
4. aorta that overrides the VSD
- Stenosis of the right ventricular outflow tract.
4Fallot.
1. Stenosis of the right ventricular outflow tract.
2…………
3. VSD
4. aorta that overrides the VSD
- right ventricular hyperthrophy
4Fallot.
1. Stenosis of the right ventricular outflow tract.
2. right ventricular hyperthrophy
3…………
4. aorta that overrides the VSD
- VSD
4Fallot.
1. Stenosis of the right ventricular outflow tract.
2. right ventricular hyperthrophy
3. VSD
4. …………
- aorta that overrides the VSD
4 fallot. Shunt? leads to what?
right to left shunt leads to early cyanosis
4fallot. What determines extent of shunting and cyanosis?
degree of stenosis.
4fallot. degree of stenosis determines what?
extent of shunting and cyanosis
4fallot. what patients does in responce to cyanosis?
Patients learn to squat in response to cyanotic spell.
4fallot. squating mechanism?
increased arterial resistance decrease shunting and allows more blood to reach the lungs.
increased arterial resistance decrease shunting and allows more blood to reach the lungs?
4 fallot. squating
4 fallot. Heart on x-ray?
,,Boot-shaped”
transposition. mechanism?
pulmonary artery arising from the left ventricle and aorta arising from left ventricle.
pulmonary artery arising from the left ventricle and aorta arising from left ventricle.?
transposition
transposition assoc with what?
maternal diabetes
transposition. symptoms?
early cyanosis.
transposition. circuits mix or not?
pulmonary and systemic circuits do not mix
transposition. what is required to do?
creation of shunt (allowing blood to mix). need for survival
transposition. what can be used to maintain PDA?
PGE – > maintain PDA until surgical rapair is performed.
transposition. results in what?
hyperthrophy of the right ventricle and atrophy of the left ventricle
hyperthrophy of the right ventricle and atrophy of the left ventricle?
transposition
Truncus arteriosus (TA). mechanism?
single large vessel arising from both ventricles
single large vessel arising from both ventricles?
Truncus arteriosus (TA).
Truncus arteriosus (TA). symptoms?
early cyanosis
Truncus arteriosus (TA). why early cyanosis?
deoxygenated blood from right ventricle mixes with oxygenated blood from left ventricle before pulmonary and aortic circulations separate.
deoxygenated blood from right ventricle mixes with oxygenated blood from left ventricle before pulmonary and aortic circulations separate.
Truncus arteriosus (TA).
Tricuspid atresia. mechanism?
tricuspid valve orifice fails to develop. right ventricle is hypoplastic.
tricuspid valve orifice fails to develop. right ventricle is hypoplastic.?
Tricuspid atresia.
Tricuspid atresia. assoc with what?
ASD, resulting in a right-to-left shunt; presents with earlyu cyanosis.
Coarctation of aorta. mechanism?
narrowing of the aorta.
Coarctation of aorta. 2 forms?
infantile and adult
Coarctation of aorta. infantile form asscow with what?
PDA.
Coarctation of aorta. in infantile where lies coarctation?
coarctation lies after (distal to) the aortic arch, but before (proximal to) the PDA.
Coarctation of aorta. infantile. symptoms?
lower extremity cyanosis in infants, often after birth
Coarctation of aorta. infantile. assoc with what?
turner syndrome
turner syndrome?
Coarctation of aorta.
Coarctation of aorta. adult. where lies coarctation?
lies after (distal to) the aortic arch
lies after (distal to) the aortic arch?
Coarctation of aorta. adult.
Coarctation of aorta. adult. symptoms?
presents as hypertension in the upper extremities and hypotension with weak pulses in the lower extremities
presents as hypertension in the upper extremities and hypotension with weak pulses in the lower extremities?
Coarctation of aorta. adult.
Coarctation of aorta. adult. collateration?
collateral circulation develops across the intercostal arteries. engorged arteries cause ,,nothcing” of ribs on x-ray
Coarctation of aorta. adult. assoc with what?
bicuspid aortic valve
bicuspid aortic valve?
Coarctation of aorta. adult.