Pathoma congenitas Teratology, transpos, TA, tricuspid, coarct 12/04 Flashcards

1
Q

4Fallot. Characterized by? 4.

A
  1. Stenosis of the right ventricular outflow tract.
  2. right ventricular hyperthrophy
  3. VSD
  4. aorta that overrides the VSD
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2
Q

4Fallot.
1…………..
2. right ventricular hyperthrophy
3. VSD
4. aorta that overrides the VSD

A
  1. Stenosis of the right ventricular outflow tract.
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3
Q

4Fallot.
1. Stenosis of the right ventricular outflow tract.
2…………
3. VSD
4. aorta that overrides the VSD

A
  1. right ventricular hyperthrophy
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4
Q

4Fallot.
1. Stenosis of the right ventricular outflow tract.
2. right ventricular hyperthrophy
3…………
4. aorta that overrides the VSD

A
  1. VSD
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5
Q

4Fallot.
1. Stenosis of the right ventricular outflow tract.
2. right ventricular hyperthrophy
3. VSD
4. …………

A
  1. aorta that overrides the VSD
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6
Q

4 fallot. Shunt? leads to what?

A

right to left shunt leads to early cyanosis

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7
Q

4fallot. What determines extent of shunting and cyanosis?

A

degree of stenosis.

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8
Q

4fallot. degree of stenosis determines what?

A

extent of shunting and cyanosis

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9
Q

4fallot. what patients does in responce to cyanosis?

A

Patients learn to squat in response to cyanotic spell.

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10
Q

4fallot. squating mechanism?

A

increased arterial resistance decrease shunting and allows more blood to reach the lungs.

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11
Q

increased arterial resistance decrease shunting and allows more blood to reach the lungs?

A

4 fallot. squating

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12
Q

4 fallot. Heart on x-ray?

A

,,Boot-shaped”

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13
Q

transposition. mechanism?

A

pulmonary artery arising from the left ventricle and aorta arising from left ventricle.

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14
Q

pulmonary artery arising from the left ventricle and aorta arising from left ventricle.?

A

transposition

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15
Q

transposition assoc with what?

A

maternal diabetes

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16
Q

transposition. symptoms?

A

early cyanosis.

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17
Q

transposition. circuits mix or not?

A

pulmonary and systemic circuits do not mix

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18
Q

transposition. what is required to do?

A

creation of shunt (allowing blood to mix). need for survival

19
Q

transposition. what can be used to maintain PDA?

A

PGE – > maintain PDA until surgical rapair is performed.

20
Q

transposition. results in what?

A

hyperthrophy of the right ventricle and atrophy of the left ventricle

21
Q

hyperthrophy of the right ventricle and atrophy of the left ventricle?

A

transposition

22
Q

Truncus arteriosus (TA). mechanism?

A

single large vessel arising from both ventricles

23
Q

single large vessel arising from both ventricles?

A

Truncus arteriosus (TA).

24
Q

Truncus arteriosus (TA). symptoms?

A

early cyanosis

25
Q

Truncus arteriosus (TA). why early cyanosis?

A

deoxygenated blood from right ventricle mixes with oxygenated blood from left ventricle before pulmonary and aortic circulations separate.

26
Q

deoxygenated blood from right ventricle mixes with oxygenated blood from left ventricle before pulmonary and aortic circulations separate.

A

Truncus arteriosus (TA).

27
Q

Tricuspid atresia. mechanism?

A

tricuspid valve orifice fails to develop. right ventricle is hypoplastic.

28
Q

tricuspid valve orifice fails to develop. right ventricle is hypoplastic.?

A

Tricuspid atresia.

29
Q

Tricuspid atresia. assoc with what?

A

ASD, resulting in a right-to-left shunt; presents with earlyu cyanosis.

30
Q

Coarctation of aorta. mechanism?

A

narrowing of the aorta.

31
Q

Coarctation of aorta. 2 forms?

A

infantile and adult

32
Q

Coarctation of aorta. infantile form asscow with what?

A

PDA.

33
Q

Coarctation of aorta. in infantile where lies coarctation?

A

coarctation lies after (distal to) the aortic arch, but before (proximal to) the PDA.

34
Q

Coarctation of aorta. infantile. symptoms?

A

lower extremity cyanosis in infants, often after birth

35
Q

Coarctation of aorta. infantile. assoc with what?

A

turner syndrome

36
Q

turner syndrome?

A

Coarctation of aorta.

37
Q

Coarctation of aorta. adult. where lies coarctation?

A

lies after (distal to) the aortic arch

38
Q

lies after (distal to) the aortic arch?

A

Coarctation of aorta. adult.

39
Q

Coarctation of aorta. adult. symptoms?

A

presents as hypertension in the upper extremities and hypotension with weak pulses in the lower extremities

40
Q

presents as hypertension in the upper extremities and hypotension with weak pulses in the lower extremities?

A

Coarctation of aorta. adult.

41
Q

Coarctation of aorta. adult. collateration?

A

collateral circulation develops across the intercostal arteries. engorged arteries cause ,,nothcing” of ribs on x-ray

42
Q

Coarctation of aorta. adult. assoc with what?

A

bicuspid aortic valve

43
Q

bicuspid aortic valve?

A

Coarctation of aorta. adult.